Mahdi Nicole, Abdelmalik Peter A, Curtis Mark, Bar Barak
Department of Neurology, Thomas Jefferson University Hospital, Philadelphia, PA 19107, USA.
Department of Pathology, Thomas Jefferson University Hospital, Philadelphia, PA 19107, USA.
Case Rep Neurol Med. 2015;2015:601706. doi: 10.1155/2015/601706. Epub 2015 Jun 9.
Objectives. Acute disseminated encephalomyelitis (ADEM) is an inflammatory demyelinating disorder that is often preceded by infection or recent vaccination. Encephalopathy and focal neurological deficits are usually manifest several weeks after a prodromal illness with rapidly progressive neurologic decline. ADEM is most commonly seen in children and young adults, in which prognosis is favorable, but very few cases have been reported of older adults with ADEM and thus their clinical course is unknown. Methods. Here we present a case of ADEM in a middle-aged adult that recovered well after treatment. Results. A 62-year-old man presented with encephalopathy and rapid neurological decline following a gastrointestinal illness. A brain MRI revealed extensive supratentorial white matter hyperintensities consistent with ADEM and thus he was started on high dose intravenous methylprednisolone. He underwent a brain biopsy showing widespread white matter inflammation secondary to demyelination. At discharge, his neurological exam had significantly improved with continued steroid treatment and four months later, he was able to perform his ADLs. Conclusions. This case of ADEM in a middle-aged adult represents an excellent response to high dose steroid treatment with a remarkable neurological recovery. Thus it behooves one to treat suspected cases of ADEM in an adult patient aggressively, as outcome can be favorable.
目的。急性播散性脑脊髓炎(ADEM)是一种炎症性脱髓鞘疾病,常先有感染或近期接种疫苗史。脑病和局灶性神经功能缺损通常在前驱疾病数周后出现,并伴有快速进展的神经功能衰退。ADEM最常见于儿童和年轻人,其预后良好,但老年ADEM患者的病例报道极少,因此其临床病程尚不清楚。方法。在此,我们报告一例中年成人ADEM患者,经治疗后恢复良好。结果。一名62岁男性在患胃肠道疾病后出现脑病和快速的神经功能衰退。脑部MRI显示幕上广泛的白质高信号,符合ADEM表现,因此开始给予大剂量静脉注射甲基强的松龙治疗。他接受了脑活检,显示继发于脱髓鞘的广泛白质炎症。出院时,经持续类固醇治疗,其神经检查有明显改善,四个月后,他能够进行日常生活活动。结论。该例中年成人ADEM对大剂量类固醇治疗反应良好,神经功能显著恢复。因此,对于成年患者疑似ADEM病例应积极治疗,因为预后可能良好。