Matteoda María Alejandra, Stefano Paola Cecilia, Bocián Marcela, Katsicas María Marta, Sala Josefina, Cervini Andrea Bettina
National Hospital of Pediatrics "Prof. Dr. Juan P. Garrahan, Buenos Aires, AR.
An Bras Dermatol. 2015 May-Jun;90(3 Suppl 1):188-90. doi: 10.1590/abd1806-4841.20153856.
Polyarteritis nodosa is a rare vasculitis in children characterized by necrotizing inflammation in small and medium size arteries. It is classified into systemic and cutaneous PAN according to the presence of systemic symptoms or visceral involvement. We describe the case of a 14-year-old girl with cutaneous Polyarteritis nodosa with an atypical clinical presentation.
结节性多动脉炎是一种儿童罕见的血管炎,其特征为中小动脉的坏死性炎症。根据是否存在全身症状或内脏受累情况,可分为系统性结节性多动脉炎和皮肤型结节性多动脉炎。我们描述了一名14岁患有皮肤型结节性多动脉炎且临床表现不典型的女孩的病例。