Poole Janet L, Huffman Matthew, Hunter Anaclaire, Mares Clare, Siegel Patricia
University of New Mexico, Occupational Therapy Graduate Program, Albuquerque, NM, USA.
University of New Mexico Hospital, Albuquerque, NM, USA.
J Hand Ther. 2015 Oct-Dec;28(4):364-7; quiz 368. doi: 10.1016/j.jht.2015.04.003. Epub 2015 Apr 30.
Descriptive, clinical measurement.
Charcot-Marie-Tooth disease (CMT) is a genetic disorder that results in demyelination or axonal degeneration in peripheral nerves. Characteristic symptoms include decreased muscle strength and sensation, particularly in the hands and feet.
Examine the reliability and validity of the Manual Ability Measure (MAM-36), a 36-item self-report questionnaire specific to hand function, in persons with CMT.
Fourteen participants with CMT completed the MAM-36 at two points one week apart. Participants were also administered performance-based tests for grip and pinch strength, dexterity, and sensation.
The test-retest intraclass correlation coefficient (ICC) for the MAM-36 was 0.96. Pearson correlation coefficients showed fair to good relationships (r = 0.41-0.64) between the MAM-36 scores and most of the performance tests.
The MAM-36 is a reliable and valid assessment tool for measuring hand function during everyday tasks in persons with CMT.
IIb.
描述性临床测量。
夏科-马里-图斯病（CMT）是一种遗传性疾病，会导致周围神经脱髓鞘或轴突变性。典型症状包括肌肉力量和感觉下降，尤其是手部和脚部。
检验手部功能特异性36项自评问卷《手动能力测量量表（MAM - 36）》在CMT患者中的信度和效度。
14名CMT患者在相隔一周的两个时间点完成了MAM - 36问卷。参与者还接受了基于表现的握力、捏力、灵活性和感觉测试。
MAM - 36的重测组内相关系数（ICC）为0.96。Pearson相关系数显示MAM - 36得分与大多数表现测试之间存在中等至良好的相关性（r = 0.41 - 0.64）。
MAM - 36是一种可靠且有效的评估工具，可用于测量CMT患者日常任务中的手部功能。
IIb。
