Marík I, Zemková D, Kubát R, Rygl M, Friedlová J
Acta Chir Orthop Traumatol Cech. 1989 Dec;56(6):507-15.
The authors present the method of predicting the body height of patients with achondroplasia in adulthood and the method of predicting shortening of the lower segment of the body as compared to the trunk. They evaluate a group of 12 patients with achondroplasia at the age from 3 to 17 years. They compare the growth curves of patients with normal Czechoslovak population and with a group of American patients suffering with achondroplasia. The application of growth curves of American patients with achondroplasia appears to be the most suitable and simple graphical method for the prediction of the body height of the Czechoslovak patients suffering from achondroplasia. The method of the prediction of dwarfism of the lower segment of the body has been developed for the purpose of the rational indication of the stepwise prolongation therapy by the compression-distraction method. Analogically it will be possible to verify the growth curves for some other bone dysplasiae presented in literature and predict dwarfism of the lower segment of the body in adulthood, e.g. in hypochondroplasia, metaphyseal chondrodysplasia of the type of Schmid, Turner syndromes, etc.
作者介绍了预测软骨发育不全患者成年后身高的方法以及预测身体下段相对于躯干缩短情况的方法。他们评估了一组年龄在3至17岁的12名软骨发育不全患者。他们将这些患者的生长曲线与正常的捷克斯洛伐克人群以及一组患有软骨发育不全的美国患者的生长曲线进行比较。对于预测捷克斯洛伐克软骨发育不全患者的身高而言，应用美国软骨发育不全患者的生长曲线似乎是最合适且简单的图表方法。为合理指导采用加压-撑开法进行的逐步延长治疗，已开发出预测身体下段侏儒症的方法。类似地，有可能验证文献中呈现的其他一些骨发育异常的生长曲线，并预测成年后身体下段的侏儒症，例如在低软骨发育不全、施密德型干骺端软骨发育不良、特纳综合征等情况中。
