Moreira-Holguin J C, Medélez-Borbonio R, Quintero-Lopez E, García-González U, Gómez-Amador J L
Neurosurgery Department, National Institute of Neurology and Neurosurgery "Manuel Velasco Suárez", Mexico City, Mexico.
Neurosurgery Department, National Institute of Neurology and Neurosurgery "Manuel Velasco Suárez", Mexico City, Mexico.
Int J Surg Case Rep. 2015;16:81-6. doi: 10.1016/j.ijscr.2015.09.022. Epub 2015 Sep 25.
Intradiploic epidermoid intracranial cysts (IEIC) derive from ectodermal cells and are covered with stratified squamous epithelium. They are extremely rare, and most common locations are in the occipital, frontal and parietal bones. They have a very slow growth and can be asymptomatic until becoming evident by the deformation produced. The treatment is based on the removal of the lesion, and subsequent histopathological confirmation.
Two cases are reported, with intracranial hypertension syndrome, which is very uncommon because of the slow growth of this type of pathology; however, decompensations occurring in the space-occupying lesions at intracranial level explain this type of clinical presentation.
The most common presentation of intracranial intradiploic epidermoid cysts (IEIC) is asymptomatically, which is made evident by the prominence at the level of the soft tissues and then presenting less frequently local pain and cephalea; rarely the size of the lesion can cause focal neurological signs.
These benign lesions, although they are of low incidence, are seen very rarely in intradiploic locations and above all, of significant size, may produce significant mass effect in patients, which was initially tolerated because of its slow growth, however, they may become decompensate and cause intracranial hypertension syndrome.
板障内表皮样颅内囊肿（IEIC）起源于外胚层细胞，被复层鳞状上皮覆盖。它们极为罕见，最常见的部位是枕骨、额骨和顶骨。其生长非常缓慢，在因产生的变形而变得明显之前可能无症状。治疗基于病变切除及随后的组织病理学确诊。
报告了两例伴有颅内高压综合征的病例，鉴于此类病变生长缓慢，这种情况非常罕见；然而，颅内占位性病变出现失代偿可解释这种临床表现类型。
颅内板障内表皮样囊肿（IEIC）最常见的表现是无症状，通过软组织层面的隆起变得明显，随后出现较少见的局部疼痛和头痛；很少情况下病变大小可导致局灶性神经体征。
这些良性病变虽然发病率低，但在板障内位置非常罕见，尤其是较大尺寸时，可能对患者产生显著的占位效应，起初因其生长缓慢而被耐受，然而，它们可能失代偿并导致颅内高压综合征。
