Kanagalingam Sivashakthi, Wyse Emily, Merbs Shannath L, Pearl Monica Smith
Department of Ophthalmology, The Johns Hopkins University School of Medicine, Baltimore, Maryland, USA.
Johns Hopkins Hospital, Baltimore, Maryland, USA.
BMJ Case Rep. 2015 Oct 5;2015:bcr2015211573. doi: 10.1136/bcr-2015-211573.
Venous-lymphatic anomalies (VLA) are rare and benign congenital lesions of the lymphatic system, composed of endothelial-lined lymphatic cysts. They are most frequently located in the region of the head and neck, and represent 4% of all orbital masses. In those patients with extensive orbital VLAs, a strong association with intracranial vascular anomalies has been reported. Factors known to suddenly increase the size of these lesions include upper respiratory tract infections or intralesional haemorrhage; however, complete spontaneous regression is rare. We report on the classic presentation of a patient with a fluctuating right orbital VLA in association with an intracranial cavernous malformation and intracranial developmental venous anomaly.
静脉-淋巴管畸形（VLA）是淋巴系统罕见的良性先天性病变，由内皮衬里的淋巴管囊肿组成。它们最常位于头颈部区域，占所有眼眶肿物的4%。据报道，在那些患有广泛眼眶VLA的患者中，与颅内血管畸形有很强的关联。已知会突然增加这些病变大小的因素包括上呼吸道感染或病灶内出血；然而，完全自发消退很少见。我们报告了一名患者的典型表现，该患者右眼眶VLA大小波动，并伴有颅内海绵状畸形和颅内发育性静脉异常。
