Acharya S K, Vashisht S, Tandon R K
Department of Gastroenterology, All India Institute of Medical Sciences, New Delhi.
Gastroenterol Jpn. 1989 Feb;24(1):75-9. doi: 10.1007/BF02774875.
Six patients with PSC have been diagnosed and followed up at a centre in Northern India for periods up to 4 years. They all presented with cholestatic jaundice and cholangitis, but one of them subsequently presented with variceal haemorrhage. Cholangiographic features were the most characteristic and included irregular narrowing and segmental dilatation of the biliary radicles giving them a beaded appearance. Treating them was most frustrating. Two of them died of hepatic encephalopathy, others have also continued to be sick during the follow-up.
印度北部一家中心已诊断出6例原发性硬化性胆管炎患者，并对其进行了长达4年的随访。他们均表现为胆汁淤积性黄疸和胆管炎，但其中1例随后出现了静脉曲张出血。胆管造影特征最为典型，包括胆管分支不规则狭窄和节段性扩张，使其呈现串珠样外观。治疗他们非常令人沮丧。其中2例死于肝性脑病，其他患者在随访期间也一直病情不佳。
