Adriano André Ricardo, Lima Tiago Silveira, Battistella Maxime, Bagot Martine
Instituto de Dermatologia Professor Rubem David Azulay, Rio de Janeiro, RJ, Brazil.
Hospital Saint Louis, Paris, France.
An Bras Dermatol. 2015 Nov-Dec;90(6):892-5. doi: 10.1590/abd1806-4841.20153807.
Granulomatous slack skin is an indolent T-cell lymphoma, considered to be a variant of mycosis fungoides. Clinically it is characterized by areas of redundant skin, wrinkled, inelastic, with variable erythema and infiltration besides a poikilodermic surface. A differential diagnosis unknown to most dermatologists is the giant cell tumor of soft tissue, which is an extremely rare low-grade sarcoma. The authors report a patient who had undergone extensive surgery because of a primary diagnosis of giant cell tumor of soft tissue, but which proved to be granulomatous slack skin after a second interventional procedure with confirmatory histopathology.
肉芽肿性皮肤松弛症是一种惰性T细胞淋巴瘤，被认为是蕈样肉芽肿的一种变体。临床上，其特征为皮肤松弛部位，皮肤起皱、缺乏弹性，除皮肤异色表面外，还有不同程度的红斑和浸润。大多数皮肤科医生并不了解的一种鉴别诊断是软组织巨细胞瘤，这是一种极为罕见的低度恶性肉瘤。作者报告了一名患者，该患者最初被诊断为软组织巨细胞瘤并接受了广泛手术，但在第二次介入手术后经组织病理学确诊为肉芽肿性皮肤松弛症。
