Garg Sumeet
J Pediatr Rehabil Med. 2016;9(1):23-9. doi: 10.3233/PRM-160358.
Scoliosis occurs in nearly all non-ambulatory children with spinal muscular atrophy (SMA) and Duchenne muscular dystrophy (DMD). Non-operative treatments have not been shown to be effective at preventing progression of scoliosis. Progressive scoliosis can impact the ability of patients to sit comfortably, be cosmetically unappealing, and in severe cases exacerbate pulmonary disease. The main goal of operative treatment is to improve sitting balance and prevent progression of scoliosis. Complication rates are high and there is little data on effect of operative treatment on quality of life in children with SMA and DMD. Comprehensive multi-disciplinary pre-operative evaluations are vital to reduce the risks of operative treatment.
脊柱侧弯几乎发生在所有非行走型脊髓性肌萎缩症(SMA)和杜氏肌营养不良症(DMD)患儿中。非手术治疗尚未被证明对预防脊柱侧弯进展有效。进行性脊柱侧弯会影响患者舒适坐姿的能力,影响美观,在严重情况下还会加重肺部疾病。手术治疗的主要目标是改善坐姿平衡并防止脊柱侧弯进展。并发症发生率很高,关于手术治疗对SMA和DMD患儿生活质量影响的数据很少。全面的多学科术前评估对于降低手术治疗风险至关重要。