Hooper Philip L, Durham Heather D, Török Zsolt, Hooper Paul L, Crul Tim, Vígh László
Division of Endocrinology, Metabolism and Diabetes, Department of Medicine, University of Colorado Anschutz Medical Campus, Aurora, CO, USA.
Department of Neurology/Neurosurgery, Montreal Neurological Institute, McGill University, Montreal, QC, Canada.
Cell Stress Chaperones. 2016 Sep;21(5):745-53. doi: 10.1007/s12192-016-0709-1. Epub 2016 Jun 9.
Networks of neuronal synapses are the fundamental basis for making and retaining memory. Reduced synapse number and quality correlates with loss of memory in dementia. Heat shock factor 1 (HSF1), the major transcription factor regulating expression of heat shock genes, plays a central role in proteostasis, in establishing and sustaining synaptic fidelity and function, and in memory consolidation. Support for this thesis is based on these observations: (1) heat shock induces improvements in synapse integrity and memory consolidation; (2) synaptic depolarization activates HSF1; (3) activation of HSF1 alone (independent of the canonical heat shock response) augments formation of essential synaptic elements-neuroligands, vesicle transport, synaptic scaffolding proteins, lipid rafts, synaptic spines, and axodendritic synapses; (4) HSF1 coalesces and activates memory receptors in the post-synaptic dendritic spine; (5) huntingtin or α-synuclein accumulation lowers HSF1 while HSF1 lowers huntingtin and α-synuclein aggregation-a potential vicious cycle; and (6) HSF1 agonists (including physical activity) can improve cognitive function in dementia models. Thus, via direct gene expression of synaptic elements, production of HSPs that assure high protein fidelity, and activation of other neuroprotective signaling pathways, HSF1 agonists could provide breakthrough therapy for dementia-associated disease.
神经元突触网络是形成和保留记忆的基本基础。突触数量和质量的减少与痴呆症中的记忆丧失相关。热休克因子1(HSF1)是调节热休克基因表达的主要转录因子,在蛋白质稳态、建立和维持突触保真度及功能以及记忆巩固中发挥核心作用。对这一论点的支持基于以下观察结果:(1)热休克可改善突触完整性和记忆巩固;(2)突触去极化激活HSF1;(3)单独激活HSF1(独立于典型的热休克反应)可增加基本突触元件——神经配体、囊泡运输、突触支架蛋白、脂筏、突触棘和轴突树突突触的形成;(4)HSF1在突触后树突棘中聚集并激活记忆受体;(5)亨廷顿蛋白或α-突触核蛋白的积累会降低HSF1,而HSF1会降低亨廷顿蛋白和α-突触核蛋白的聚集——这是一个潜在的恶性循环;(6)HSF1激动剂(包括体育活动)可改善痴呆模型中的认知功能。因此,通过突触元件的直接基因表达、确保高蛋白质保真度的热休克蛋白的产生以及其他神经保护信号通路的激活,HSF1激动剂可为痴呆相关疾病提供突破性治疗。