Nakamura T, Sawayama T, Hasegawa K, Nezuo S, Tadaoka S, Nakao M, Kakumae S, Kawahara Y, Inoue S, Takatori K
Kokyu To Junkan. 1989 Mar;37(3):347-50.
A 46-year-old man was hospitalized with paroxysmal headache and chest discomfort. His blood pressure varied, occasionally being up to 300/160 mmHg. Cardiac examination revealed a decrescendo type of diastolic murmur (aortic regurgitation) and S4 gallop. Both blood and urine catecholamine levels were extremely high. Electrocardiogram and echocardiogram showed severe left ventricular hypertrophy pattern presenting hypertrophic cardiomyopathic changes. The phonocardiogram showed marked Hegglin syndrome (QT; 450 msec and QII; 310 msec). Right adrenal tumor, pheochromocytoma was found on the abdominal CT scanning and 131I-metaiodobenzylguanidine (MIBG). In the post-operative period, Hegglin syndrome was completely abolished (QT; 360 msec and QII; 345 msec,), and also electrocardiographic left ventricular hypertrophy pattern improved immediately after surgical removal of the pheochromocytoma.
一名46岁男性因阵发性头痛和胸部不适入院。他的血压波动不定，偶尔高达300/160 mmHg。心脏检查发现递减型舒张期杂音（主动脉瓣关闭不全）和S4奔马律。血、尿儿茶酚胺水平均极高。心电图和超声心动图显示严重左心室肥厚模式，呈现肥厚型心肌病改变。心音图显示明显的赫格利综合征（QT；450毫秒，QII；310毫秒）。腹部CT扫描和131I-间碘苄胍（MIBG）检查发现右肾上腺肿瘤，即嗜铬细胞瘤。术后，赫格利综合征完全消失（QT；360毫秒，QII；345毫秒），切除嗜铬细胞瘤后心电图左心室肥厚模式也立即改善。
