Yun Dong-Ju, Hwang Byeong-Wook, Kim Dae Jin, Lee Sang-Ho
Department of Neurosurgery, Spine Health Wooridul Hospital (SHWH), Busan, Korea.
Department of Neurosurgery, Spine Health Wooridul Hospital (SHWH), Busan, Korea.
World Neurosurg. 2016 Sep;93:489.e1-5. doi: 10.1016/j.wneu.2016.06.088. Epub 2016 Jun 29.
Abnormalities of the posterior arches of the upper and middle cervical spine that can cause myelopathy are rare, and no reports of such defects at the thoracic spinal level have been published.
A 29-year-old male patient reported right arm weakness and pain for 1 year. Magnetic resonance imaging of the cervical spine showed spinal canal stenosis at the C3-4 and C4-5 levels, as well as a posterior arch defect at the C2, 3, and 4 levels that was compressing the spinal cord. Three-dimensional cervical computed tomography (CT) showed that the spinous process and a piece of lamina were fused at each of the posterior C2, 3, and 4 levels, producing a free-floating bony structure. Spina bifida occulta was observed at C1. Osseous formation had failed between the lateral mass and spinous process at the C2 and C3 levels bilaterally, and the C4 level unilaterally. Three-dimensional thoracolumbar CT showed blocked vertebrae and spinous process fusion at T11 and T12. Osseous formation had failed between the lamina and spinous process at the T11 level unilaterally, and the T12 level bilaterally. The free-floating bony structure was successfully removed surgically.
A posterior arch defect of the upper and middle cervical spine leading to myelopathy combined with the same defect at the thoracic spine is a rare disease. If this congenital defect is detected at any spinal level, whole-spine CT can be helpful for accurately diagnosing the congenital anomaly.
可导致脊髓病的上颈椎和中颈椎后弓异常较为罕见,且尚无关于胸段脊柱此类缺陷的报道。
一名29岁男性患者报告右臂无力和疼痛1年。颈椎磁共振成像显示C3 - 4和C4 - 5水平椎管狭窄,以及C2、3和4水平的后弓缺陷压迫脊髓。颈椎三维计算机断层扫描(CT)显示C2、3和4水平后方每个棘突和一块椎板融合,形成一个游离的骨性结构。C1处观察到隐性脊柱裂。双侧C2和C3水平以及单侧C4水平侧块与棘突之间骨形成失败。胸腰段三维CT显示T11和T12椎体阻滞和棘突融合。单侧T11水平以及双侧T12水平椎板与棘突之间骨形成失败。手术成功切除了游离的骨性结构。
上颈椎和中颈椎后弓缺陷导致脊髓病并合并胸段脊柱相同缺陷是一种罕见疾病。如果在任何脊柱水平检测到这种先天性缺陷,全脊柱CT有助于准确诊断先天性异常。