Kogiso Tomomi, Hashimoto Etsuko, Ito Taito, Hara Toshifumi, Ikarashi Yuichi, Kodama Kazuhisa, Taniai Makiko, Torii Nobuyuki, Yoshinaga Kentaro, Morita Satoru, Takahashi Yutaka, Tanaka Junji, Sakai Shuji, Yamamoto Masakazu, Tokushige Katsutoshi
Institute of Gastroenterology, Department of Internal Medicine, Tokyo Women's Medical University, Japan.
Intern Med. 2016;55(20):2957-2963. doi: 10.2169/internalmedicine.55.7087. Epub 2016 Oct 15.
A 56-year-old man was diagnosed with aplastic anemia and paroxysmal nocturnal hemoglobinuria at 43 years of age and treatment with cyclosporin A was started. Liver cirrhosis, ascites, and thrombus in the hepatic veins were found at 56 years of age and Budd-Chiari syndrome (BCS) was diagnosed according to angiography findings. He was treated with diuretics and paracentesis was performed several times, but with limited efficacy. A Denver peritoneovenous shunt (PVS) was inserted into the right jugular vein; his ascites and renal function improved immediately and his general condition has remained good for 12 months since starting the above treatment regimen. A PVS is a treatment option for ascites due to BCS.
一名56岁男性在43岁时被诊断为再生障碍性贫血和阵发性夜间血红蛋白尿，并开始使用环孢素A进行治疗。56岁时发现肝硬化、腹水和肝静脉血栓形成，根据血管造影结果诊断为布加综合征（BCS）。他接受了利尿剂治疗，并多次进行腹腔穿刺，但效果有限。在右颈静脉插入了Denver腹腔静脉分流术（PVS）；自开始上述治疗方案以来，他的腹水和肾功能立即得到改善，并且他的一般状况在12个月内一直保持良好。PVS是治疗BCS所致腹水的一种选择。
