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营养不良性大疱性表皮松解症患者的牙科和麻醉挑战

Dental and Anaesthetic Challenges in a Patient with Dystrophic Epidermolysis Bullosa.

作者信息

Al-Abadi Ali, Al-Azri Salah A, Bakathir Abdulaziz, Al-Riyami Yusra

机构信息

Department of Anaesthesia & ICU, Sultan Qaboos University Hospital, Muscat, Oman.

Oral & Maxillofacial Surgery Residency Program, Oman Medical Specialty Board, Muscat, Oman.

出版信息

Sultan Qaboos Univ Med J. 2016 Nov;16(4):e495-e499. doi: 10.18295/squmj.2016.16.04.016. Epub 2016 Nov 30.

Abstract

Epidermolysis bullosa is a group of rare genetic disorders characterised by skin and mucous membrane fragility and systemic manifestations of variable severity. We report a case of dystrophic epidermolysis bullosa in an 18-year-old male patient who presented to the Department of Oral Health at Sultan Qaboos University Hospital, Muscat, Oman, in 2015 with recurrent dental pain and infections. Due to the poor dental status of the patient and anticipated operative difficulties due to and limited mouth opening, the patient underwent full dental clearance under general anaesthesia. This article discusses the dental and anaesthetic challenges encountered during the management of this patient and provides a brief literature review.

摘要

大疱性表皮松解症是一组罕见的遗传性疾病,其特征为皮肤和黏膜脆弱以及严重程度各异的全身表现。我们报告一例营养不良型大疱性表皮松解症病例,患者为一名18岁男性,2015年因反复牙痛和感染就诊于阿曼马斯喀特苏丹卡布斯大学医院口腔健康科。由于患者牙齿状况不佳,且因[此处原文缺失相关内容]和张口受限预计手术困难,患者在全身麻醉下接受了全口牙拔除。本文讨论了该患者治疗过程中遇到的牙科和麻醉挑战,并提供了简要的文献综述。

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