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糖原性肝病，1型糖尿病控制不佳时复发性肝炎的一个未被充分诊断的病因。

Glycogenic hepatopathy, an underdiagnosed cause of relapsing hepatitis in uncontrolled type 1 diabetes mellitus.

作者信息

Al Sarkhy Ahmed A, Zaidi Zafar A, Babiker Amir M

机构信息

Gastroenterology Unit, Pediatric Department, King Khalid University Hospital, King Saud University, Riyadh, Kingdom of Saudi Arabia. E-mail.

出版信息

Saudi Med J. 2017 Jan;38(1):89-92. doi: 10.15537/smj.2017.1.15934.

DOI:10.15537/smj.2017.1.15934
PMID:28042636
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5278071/
Abstract

Glycogenic hepatopathy is a rare condition that causes significant hepatomegaly and elevated liver enzyme levels in uncontrolled type 1 diabetic patients. It develops due to excessive accumulation of glycogen in the hepatocytes. It is typically reversible with good glycemic control and rarely progresses to mild fibrosis, but not cirrhosis.

摘要

糖原性肝病是一种罕见的病症，在未得到控制的1型糖尿病患者中会导致明显的肝脏肿大和肝酶水平升高。它是由于肝细胞中糖原过度积累而发生的。通过良好的血糖控制，它通常是可逆的，很少进展为轻度纤维化，但不会发展为肝硬化。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/14ea/5278071/e00fb049351f/SaudiMedJ-38-89-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/14ea/5278071/e00fb049351f/SaudiMedJ-38-89-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/14ea/5278071/e00fb049351f/SaudiMedJ-38-89-g001.jpg

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