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依维莫司治疗伴下腔静脉血栓的结节性硬化症相关肾血管平滑肌脂肪瘤的疗效:一例报告

Efficacy of Everolimus for Treating Renal Angiomyolipoma with Inferior Vena Cava Thrombus Associated with Tuberous Sclerosis: A Case Report.

作者信息

Ikarashi Daiki, Mue Yoshiharu, Shiomi Ei, Takayama Misato, Kato Renpei, Kato Yoichiro, Ishida Kazuyuki, Abe Takaya, Sugai Tamotsu, Obara Wataru

机构信息

Department of Urology, Iwate Medical University School of Medicine, Iwate, Japan.

Department of Pathology, Iwate Medical University School of Medicine, Iwate, Japan.

出版信息

Urol Case Rep. 2017 Jan 5;11:11-13. doi: 10.1016/j.eucr.2016.12.003. eCollection 2017 Feb.

Abstract

Here we report a case of 57-year-old woman with renal angiomyolipoma associated with tuberous sclerosis complex involving inferior vena cava thrombus. We could perform less invasive nephrectomy with thrombectomy because everolimus administration reduced the inferior vena cava thrombus. To the best of our knowledge, this is the first report the use of everolimus before performing surgery to treat renal angiomyolipoma with inferior vena cava thrombus.

摘要

在此,我们报告一例57岁女性,患有与结节性硬化症相关的肾血管平滑肌脂肪瘤,并累及下腔静脉血栓形成。由于依维莫司的使用使下腔静脉血栓缩小,我们得以实施创伤较小的肾切除术并进行血栓切除术。据我们所知,这是首例在手术治疗伴有下腔静脉血栓的肾血管平滑肌脂肪瘤之前使用依维莫司的报告。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/27dd/5220258/1a0cf1f5a376/gr1.jpg

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