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依维莫司治疗伴下腔静脉血栓的结节性硬化症相关肾血管平滑肌脂肪瘤的疗效:一例报告

Efficacy of Everolimus for Treating Renal Angiomyolipoma with Inferior Vena Cava Thrombus Associated with Tuberous Sclerosis: A Case Report.

作者信息

Ikarashi Daiki, Mue Yoshiharu, Shiomi Ei, Takayama Misato, Kato Renpei, Kato Yoichiro, Ishida Kazuyuki, Abe Takaya, Sugai Tamotsu, Obara Wataru

机构信息

Department of Urology, Iwate Medical University School of Medicine, Iwate, Japan.

Department of Pathology, Iwate Medical University School of Medicine, Iwate, Japan.

出版信息

Urol Case Rep. 2017 Jan 5;11:11-13. doi: 10.1016/j.eucr.2016.12.003. eCollection 2017 Feb.

DOI:10.1016/j.eucr.2016.12.003
PMID:28083476
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5220258/
Abstract

Here we report a case of 57-year-old woman with renal angiomyolipoma associated with tuberous sclerosis complex involving inferior vena cava thrombus. We could perform less invasive nephrectomy with thrombectomy because everolimus administration reduced the inferior vena cava thrombus. To the best of our knowledge, this is the first report the use of everolimus before performing surgery to treat renal angiomyolipoma with inferior vena cava thrombus.

摘要

在此,我们报告一例57岁女性,患有与结节性硬化症相关的肾血管平滑肌脂肪瘤,并累及下腔静脉血栓形成。由于依维莫司的使用使下腔静脉血栓缩小,我们得以实施创伤较小的肾切除术并进行血栓切除术。据我们所知,这是首例在手术治疗伴有下腔静脉血栓的肾血管平滑肌脂肪瘤之前使用依维莫司的报告。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/27dd/5220258/c5b128fa2846/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/27dd/5220258/1a0cf1f5a376/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/27dd/5220258/b8377378b73c/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/27dd/5220258/c5b128fa2846/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/27dd/5220258/1a0cf1f5a376/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/27dd/5220258/b8377378b73c/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/27dd/5220258/c5b128fa2846/gr3.jpg

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本文引用的文献

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Aggressive Renal Angiomyolipoma of the Lipomatous Variant With Inferior Vena Cava Thrombus: A Case Report and Review of the Literature.伴有下腔静脉血栓形成的脂肪型侵袭性肾血管平滑肌脂肪瘤:一例报告并文献复习
Urol Case Rep. 2013 Dec 25;2(1):9-11. doi: 10.1016/j.eucr.2013.11.009. eCollection 2014 Jan.
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Invasive Epithelioid Angiomyolipoma with Tumor Thrombus in the Inferior Vena Cava: A Case Report and Literature Review.下腔静脉内伴有肿瘤血栓的侵袭性上皮样血管平滑肌脂肪瘤:一例报告及文献复习
Urol Int. 2017;98(1):120-124. doi: 10.1159/000434648. Epub 2015 Jul 3.
3
Everolimus for angiomyolipoma associated with tuberous sclerosis complex or sporadic lymphangioleiomyomatosis (EXIST-2): a multicentre, randomised, double-blind, placebo-controlled trial.
依维莫司治疗伴下腔静脉血栓形成的散发性肾血管平滑肌脂肪瘤的疗效:病例报告
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4
Diagnostic features of tuberous sclerosis complex: case report and literature review.结节性硬化症复合体的诊断特征:病例报告与文献综述
Quant Imaging Med Surg. 2022 Jan;12(1):846-861. doi: 10.21037/qims-21-412.
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Preoperative inferior vena cava filter implantation to prevent pulmonary fat embolism in a patient showing renal angiomyolipoma extension into the renal vein: A case report and literature review.术前植入下腔静脉滤器以预防肾血管平滑肌脂肪瘤延伸至肾静脉患者的肺脂肪栓塞:一例报告及文献综述
J Rural Med. 2018 Nov;13(2):181-184. doi: 10.2185/jrm.2976. Epub 2018 Nov 29.
依维莫司治疗结节性硬化症相关的血管平滑肌脂肪瘤或散发性淋巴管平滑肌瘤病(EXIST-2):一项多中心、随机、双盲、安慰剂对照试验。
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