Anuradha S, Fanai Vanlalmalsawmdawngliana
Department of Medicine, Maulana Azad Medical College and Associated Hospitals, New Delhi 110002, India.
Case Rep Neurol Med. 2016;2016:5839761. doi: 10.1155/2016/5839761. Epub 2016 Dec 21.
Hirayama disease, also known as monomelic amyotrophy (MMA), is a rare cervical myelopathy that manifests itself as a self-limited, asymmetrical, slowly progressive atrophic weakness of the forearms and hands predominantly in young males. The forward displacement of the posterior dura of the lower cervical dural canal during neck flexion has been postulated to lead to lower cervical cord atrophy with asymmetric flattening. We report a case of Hirayama disease in a 25-year-old Indian man presenting with gradually progressive asymmetrical weakness and wasting of both hands and forearms along with unusual features of autonomic dysfunction and upper motor neuron lesion.
平山病，也称为单肢肌萎缩症（MMA），是一种罕见的颈髓病，主要表现为年轻男性前臂和手部自限性、不对称、缓慢进展的萎缩性肌无力。颈部屈曲时下颈段硬脊膜管后硬膜向前移位被认为会导致下颈段脊髓萎缩并伴有不对称扁平。我们报告一例25岁印度男性平山病病例，该患者表现为双手和前臂逐渐进展的不对称肌无力和萎缩，同时伴有自主神经功能障碍和上运动神经元损害的异常特征。
