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伴重症肌无力的多发性胸腺瘤

Multiple Thymoma with Myasthenia Gravis.

作者信息

Seo Dong Hyun, Cho Sukki

机构信息

Department of Thoracic and Cardiovascular Surgery, Seoul National University Bundang Hospital.

Department of Thoracic and Cardiovascular Surgery, Seoul National University Bundang Hospital; Department of Thoracic and Cardiovascular Surgery, Seoul National University College of Medicine.

出版信息

Korean J Thorac Cardiovasc Surg. 2017 Feb;50(1):68-70. doi: 10.5090/kjtcs.2017.50.1.68. Epub 2017 Feb 5.

DOI:10.5090/kjtcs.2017.50.1.68
PMID:28180109
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5295489/
Abstract

The actual incidence of multiple thymoma is unknown and rarely reported because it remains controversial whether the cases represent a disease of multicentric origin or a disease resulting from intrathymic metastasis. In this case, a patient underwent total thymectomy for multiple thymoma with myasthenia gravis via bilateral video-assisted thoracic surgery. A well-encapsulated multinodular cystic mass, measuring 57 mm×50 mm×22 mm in the right lobe of the thymus, and a well-encapsulated mass, measuring 32 mm×15 mm×14 mm in the left lobe, were found. Both tumors were type B2 thymoma. Few cases of multiple thymoma with myasthenia gravis have ever been reported in the literature. We report a case of synchronous multiple thymoma associated with myasthenia gravis.

摘要

多原发性胸腺瘤的实际发病率尚不清楚,且鲜有报道,因为这些病例究竟代表多中心起源的疾病还是胸腺内转移所致的疾病仍存在争议。在此病例中,一名患有重症肌无力的多原发性胸腺瘤患者通过双侧电视辅助胸腔镜手术接受了全胸腺切除术。在胸腺右叶发现一个边界清晰的多结节囊性肿块,大小为57 mm×50 mm×22 mm,在左叶发现一个边界清晰的肿块,大小为32 mm×15 mm×14 mm。两个肿瘤均为B2型胸腺瘤。文献中很少有关于伴有重症肌无力的多原发性胸腺瘤病例的报道。我们报告一例伴有重症肌无力的同步性多原发性胸腺瘤病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/75fc/5295489/9dc305fce98e/kjtcvs-50-068f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/75fc/5295489/be056ffe5b12/kjtcvs-50-068f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/75fc/5295489/9dc305fce98e/kjtcvs-50-068f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/75fc/5295489/be056ffe5b12/kjtcvs-50-068f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/75fc/5295489/9dc305fce98e/kjtcvs-50-068f2.jpg

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引用本文的文献

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Zhongguo Fei Ai Za Zhi. 2018 Apr 20;21(4):265-268. doi: 10.3779/j.issn.1009-3419.2018.04.05.

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