Benjouad Ibtihale, Taam Ikram, Ataouna Khaoula El, Mahi Mohamed, Amil Touriya, Saouab Rachida
Service d'Imagerie Médicale, Hôpital Militaire d'Instruction Mohammed V, Rabat, Maroc.
Service de Pneumologie, Hôpital Militaire d'Instruction Mohammed V, Rabat, Maroc.
Pan Afr Med J. 2016 Sep 28;25:37. doi: 10.11604/pamj.2016.25.37.10545. eCollection 2016.
Scimitar syndrome or veino-lobaire syndrome (term coined by Felson) is a very rare disease characterized by the combination of cardiopulmonary anomalies, in particular an anomalous right pulmonary venous return, located mostly in the inferior vena cava. We here report the original case of a 6-month-old female infant presenting with acute dyspnea. The diagnosis was suspected on the basis of thoracic radiograph and was confirmed by tomodensitometry which showed a large single right pulmonary vein draining into the right atrium associated with dextrocardia and pulmonary sequestration. The prognosis was based on the size of the left-right shunt and related malformations.
弯刀综合征或肺叶静脉综合征（由费尔森提出的术语）是一种非常罕见的疾病，其特征是心肺异常合并存在，特别是右肺静脉回流异常，主要位于下腔静脉。我们在此报告一例6个月大急性呼吸困难女婴的原始病例。根据胸部X光片怀疑诊断，并通过计算机断层扫描证实，该扫描显示一条粗大的单一右肺静脉汇入右心房，伴有右位心和肺隔离症。预后取决于左右分流的大小及相关畸形。
