Holt Peter D, Berdon Walter E, Marans Zvi, Griffiths Sylvia, Hsu Daphne
Department of Radiology, Columbia University, College of Physicians and Surgeons, Children's Hospital of New York-Presbyterian, Babies Hospital 3N, 3959 Broadway, New York, NY 10032, USA.
Pediatr Radiol. 2004 May;34(5):409-13. doi: 10.1007/s00247-004-1149-0. Epub 2004 Feb 11.
Scimitar vein draining to the left atrium is the rarest of the pulmonary venolobar anomalies with less than a dozen reported cases. A case is reported of a patient whose plain film radiographic findings showed a typical scimitar vein but whose echocardiography showed normal pulmonary venous drainage. Cardiac catheterization confirmed drainage of the scimitar vein to the left atrium and systemic arterial supply which was embolized. The case described is used to review the history of "scimitar syndrome" with reflections on the significant contributions of Halasz and colleagues, who in 1956 helped define the anatomy, and Neill and colleagues, who in 1960 described the familial occurrence and clinical spectrum of the condition.
引流至左心房的弯刀状静脉是肺静脉叶异常中最罕见的类型,报告病例少于12例。本文报告了1例患者,其胸部X线平片表现显示典型的弯刀状静脉,但超声心动图显示肺静脉引流正常。心导管检查证实弯刀状静脉引流至左心房并有体循环动脉供血,已对其进行栓塞。本文通过该病例回顾了“弯刀综合征”的历史,并对哈拉斯及其同事(他们在1956年帮助明确了解剖结构)以及尼尔及其同事(他们在1960年描述了该病的家族性发病情况和临床谱)所做出的重大贡献进行了思考。