Safari Mohammad Taghi, Shahrokh Shabnam, Miri Mohammad Bagher, Foroughi Forough, Sadeghi Amir
Gastroenterology and Liver Diseases Research Center, Research Institute for Gastroenterology and Liver Diseases, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
Basic and Molecular Epidemiology of Gastrointestinal Disorders Research Center, Research Institute for Gastroenterology and Liver Diseases, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
Gastroenterol Hepatol Bed Bench. 2016 Dec;9(Suppl1):S88-S92.
Hepatobiliary cystadenomas (HBC) is a rare neoplasm which comprising less than one percent of liver cystic neoplasms. Although it's known as a benign tumor, but they have a potential for neoplastic transformation. Making a proper diagnosis and ruling out of other differential diagnosis is important because of different treatment. In the present study, we described a case of HBC manifested as idiopathic dominant biliary stricture in common hepatic duct (CHD), on the basis of spiral CT scan and MRI, and elevated CA19-9. With a probable diagnosis of malignant biliary stricture, she underwent ERCP and cholangioscopy that were non-diagnostic and final diagnosis was made surgically. HBCs usually found incicentally as a cystic lesion and biliary stricture without visible cyst in imaging like that seen in cholangiocarcinoma is very unlikely. In truth, this patient is an unusual manifestation of one rare disease.
肝内胆管囊腺瘤（HBC）是一种罕见的肿瘤，占肝囊性肿瘤的比例不到1%。尽管它被认为是一种良性肿瘤，但它们有发生肿瘤转化的可能性。由于治疗方法不同，做出正确诊断并排除其他鉴别诊断很重要。在本研究中，我们描述了一例HBC病例，该病例表现为肝总管（CHD）特发性显性胆管狭窄，基于螺旋CT扫描和MRI以及CA19-9升高。由于可能诊断为恶性胆管狭窄，她接受了内镜逆行胰胆管造影（ERCP）和胆管镜检查，但未得出诊断结果，最终通过手术做出了诊断。HBC通常偶然发现为囊性病变，而像胆管癌那样在影像学上没有可见囊肿的胆管狭窄非常罕见。事实上，该患者是一种罕见疾病的不寻常表现。
