Fontan手术在先天性矫正型大动脉转位治疗中的作用。
The role of the Fontan operation in the treatment of congenitally corrected transposition of the great arteries.
作者信息
Karl Tom R
机构信息
Department of Paediatric Cardiac Surgery, Queensland Paediatric Cardiac Service, Mater Children's Hospital, Brisbane, Australia.
出版信息
Ann Pediatr Cardiol. 2011 Jul;4(2):103-10. doi: 10.4103/0974-2069.84634.
Abstract
Congenitally corrected transposition of the great arteries (ccTGA) is a complex cardiac anomaly with an unfavorable natural history. Surgical treatment has been available for over 50 years. Initial procedures used for ccTGA did not correct atrio-ventricular discordance, leaving the right ventricle in systemic position. In the past two decades anatomic repair has been considered to be a better option. Many cases subjected to anatomic repairs would also be suitable for the Fontan strategy, which probably has a lower initial risk. The rationale for use of the Fontan operation in management of congenitally corrected transposition is discussed in this review, with comparisons to other strategies.
摘要
先天性矫正型大动脉转位（ccTGA）是一种复杂的心脏畸形，其自然病史不佳。外科治疗已有50多年的历史。最初用于ccTGA的手术并未纠正房室不一致，使右心室处于体循环位置。在过去二十年中，解剖修复被认为是更好的选择。许多接受解剖修复的病例也适合采用Fontan策略，该策略可能初始风险较低。本文综述了在先天性矫正型大动脉转位管理中使用Fontan手术的理论依据，并与其他策略进行了比较。
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