Ajmera Prakash, Medep Vikas
NH Malla Reddy Narayana Multispeciality Hospital, Hyderabad, Telangana 500055, India.
Case Rep Med. 2017;2017:7565870. doi: 10.1155/2017/7565870. Epub 2017 Feb 9.
Congenitally corrected transposition of the great arteries (CCTGA) is rare form of congenital heart diseases. It may be present with or without associated anomalies. Patients with CCTGA are usually diagnosed at early stages of life due to associated anomalies, but they may even remain asymptomatic till later decades of their life. We report a case of a 42-year-old man who presented at neurosurgery department with dizziness, seizures, and loss of consciousness, in whom isolated CCTGA was discovered incidentally. Further investigation depicted right ventricular hypertrophy, mild valvular regurgitation, mildly dilated pulmonary artery, low heart rate with AV dissociation, and third-degree heart block. These indicated for implantation of permanent pacemaker into the patient. The implantation of VVI mode pacemaker was uneventful and the patient is being followed up in the past eight months in favorable condition.
先天性矫正型大动脉转位（CCTGA）是一种罕见的先天性心脏病。它可能伴有或不伴有相关异常。患有CCTGA的患者通常由于相关异常在生命早期被诊断出来，但他们甚至可能在生命的后几十年都没有症状。我们报告一例42岁男性患者，因头晕、癫痫发作和意识丧失就诊于神经外科，偶然发现孤立性CCTGA。进一步检查显示右心室肥厚、轻度瓣膜反流、轻度扩张的肺动脉、伴有房室分离的低心率和三度房室传导阻滞。这些提示该患者需要植入永久性起搏器。VVI模式起搏器植入过程顺利，患者在过去八个月中一直处于良好状态并接受随访。
