Hur Kevin, Liu Changxing, Koempel Jeffrey A
Caruso Department of Otolaryngology, Keck School of Medicine, University of Southern California, Los Angeles, CA 90033, USA.
Division of Otolaryngology, Head and Neck Surgery, Children's Hospital Los Angeles, Los Angeles, CA 90027, USA.
Case Rep Otolaryngol. 2017;2017:1453097. doi: 10.1155/2017/1453097. Epub 2017 Feb 21.
Rosai-Dorfman disease is a rare histiocytic proliferative disorder of unknown etiology typically characterized by cervical lymphadenopathy. Extranodal involvement often manifests in the head and neck region. We present a 10-year-old male who presented to our hospital with left epiphora from an aggressive paranasal mass invading the left orbit with osseous destruction. The mass was surgically biopsied and debulked with histopathological examination revealing Rosai-Dorfman disease. Although rarely found in the sinuses, Rosai-Dorfman disease should be considered when evaluating sinonasal masses.
罗萨伊-多夫曼病是一种病因不明的罕见组织细胞增生性疾病，典型表现为颈部淋巴结病。结外受累常表现在头颈部区域。我们报告一名10岁男性，因侵袭性鼻窦肿物侵犯左侧眼眶并伴有骨质破坏，导致左眼溢泪，前来我院就诊。该肿物经手术活检并部分切除，组织病理学检查显示为罗萨伊-多夫曼病。尽管罗萨伊-多夫曼病在鼻窦中很少见，但在评估鼻窦肿物时应考虑到该病。
