ALSaleh Nourah, ALwadie Hadeel, Gari Abdulrahim
Bachelor degree of medicine and general surgery (MBBS), Umm Al-Qura University, Makkah, Saudi Arabia.
Medical Intern, King Khalid University, Abha, Saudi Arabia.
J Surg Case Rep. 2017 Apr 27;2017(4):rjx080. doi: 10.1093/jscr/rjx080. eCollection 2017 Apr.
Embryonal Rhabdomyosarcoma 'Botryoid Type' is a rare soft tissue tumor that arises within the wall of the bladder or vagina and seen almost exclusively in infants. Treatment is combination of surgery with adjuvants chemotherapy and radiotherapy. We report a case of an 18-month-old Saudi girl presented with history of abdo-pelvic mass, bleeding per vagina and a mass protruding through the introitus. Computed tomography (CT) done reveling large heterogeneous pelvic mass arising from the uterus, biopsy of mass confirmed the diagnosis (sarcomabotryoidal). The patient received multiple cycles of combination chemotherapy as a neoadjuvant treatment then underwent total abdominal hysterectomy with upper vaginectomy. Postoperatively, the patient received more cycles of chemotherapy. CT scan for post-treatment evaluation was done and showed no evidence of local recurrence or distant metastasis. Currently, she is disease-free on remission with no complains.
葡萄状胚胎性横纹肌肉瘤是一种罕见的软组织肿瘤，发生于膀胱或阴道壁内，几乎仅见于婴儿。治疗方法是手术联合辅助化疗和放疗。我们报告一例18个月大的沙特女孩，有腹盆腔肿块、阴道出血及肿物自阴道口突出的病史。计算机断层扫描（CT）显示子宫有一个大的不均质盆腔肿块，肿块活检确诊诊断（葡萄状肉瘤）。患者接受了多个周期的联合化疗作为新辅助治疗，然后接受了全腹子宫切除术及上段阴道切除术。术后，患者接受了更多周期的化疗。进行了治疗后评估的CT扫描，未显示局部复发或远处转移的证据。目前，她处于疾病缓解期，无不适主诉。
