Bruschini Luca, Ciabotti Annalisa, De Vito Andrea, Forli Francesca, Cambi Christina, Ciancia Eugenio Maria, Berrettini Stefano
Ear, Nose, Throat (ENT) Audiology and Phoniatry Unit, University Hospital of Pisa, Pisa, Italy.
Department of Pathology, University Hospital of Pisa, Pisa, Italy.
Am J Case Rep. 2017 May 11;18:520-524. doi: 10.12659/ajcr.902900.
BACKGROUND Ceruminous glands are modified apocrine glands, situated in the external auditory canal, that, together with sebaceous glands, produce cerumen, better known as ear wax. The neoplastic transformation of these structures is very rare and there have been few cases reported in the literature. CASE REPORT Syringocystadenoma papilliferum is one of the rarest tumors among benign tumors arising from the ceruminous glands. We here report the case of a 72-year-old man with a lesion histologically documented as a syringocystadenoma papilliferum and we review the literature, focusing our attention on clinical features and treatment options of benign glandular tumors arising from the external auditory canal. CONCLUSIONS Syringocystadenoma papilliferum is a rare benign tumor of the ceruminous glands of the external ear canal. Excision biopsy is mandatory for the diagnosis and is the best treatment.
耵聍腺是一种特殊的顶泌汗腺，位于外耳道，与皮脂腺共同分泌耵聍，即俗称的耳垢。这些结构的肿瘤性转化非常罕见，文献报道的病例较少。病例报告：乳头状囊腺瘤是源自耵聍腺的良性肿瘤中最罕见的肿瘤之一。我们在此报告一例72岁男性患者，其病变经组织学证实为乳头状囊腺瘤，并对文献进行复习，重点关注外耳道良性腺性肿瘤的临床特征和治疗选择。结论：乳头状囊腺瘤是外耳道耵聍腺的一种罕见良性肿瘤。切除活检是诊断的必要手段，也是最佳治疗方法。
