Wilde Lucy, Oliver Chris
Cerebra Centre for Neurodevelopmental Disorders, School of Psychology, University of Birmingham, Birmingham, B15 2TT, UK.
J Autism Dev Disord. 2017 Aug;47(8):2602-2609. doi: 10.1007/s10803-017-3140-2.
Everyday executive function (EF) was examined in Smith-Magenis syndrome (SMS), associated with high risk of behaviour disorder, and Down syndrome (DS), associated with relatively low risk of behaviour disorder. Caregivers of 13 children with SMS and 17 with DS rated everyday EF using the Behavioral Rating Inventory of Executive Functioning-Preschool. Greater everyday EF deficits relative to adaptive ability were evident in SMS than in DS. The SMS profile of everyday EF abilities was relatively uniform; in DS emotional control strengths and working memory weaknesses were evident. Findings implicate broad everyday EF difficulties in SMS compared to DS, corresponding with increased rates of behaviour disorder in SMS. Findings further suggest that everyday EF profiles may, in part, be syndrome related.
对患有行为障碍高风险的史密斯-马吉尼斯综合征（SMS）和行为障碍风险相对较低的唐氏综合征（DS）儿童的日常执行功能（EF）进行了研究。13名SMS患儿和17名DS患儿的照料者使用《执行功能学前行为评定量表》对日常EF进行评分。与DS患儿相比，SMS患儿相对于适应能力的日常EF缺陷更为明显。SMS患儿日常EF能力的表现相对较为一致；而DS患儿则表现出情绪控制优势和工作记忆弱点。研究结果表明，与DS患儿相比，SMS患儿存在广泛的日常EF困难，这与SMS患儿行为障碍发生率的增加相一致。研究结果进一步表明，日常EF表现可能部分与综合征有关。
