Mansi Meha, Mahajan Nidhi, Mahana Sonam, Gupta C R, Mohta Anup
Department of Pathology, Chacha Nehru Bal Chikitsalaya, New Delhi, India.
Department of Pediatric Surgery, Chacha Nehru Bal Chikitsalaya, New Delhi, India.
Case Rep Gastrointest Med. 2017;2017:7294896. doi: 10.1155/2017/7294896. Epub 2017 Apr 26.
Mediastinal enteric duplication cysts are a rare congenital malformation encountered mainly in neonates and infants. It is a distinct entity within the family of foregut duplication cysts. It can present with respiratory distress due to mass effect and hence surgical excision is the preferred treatment. Histologically, it is characterised by a double layered smooth muscle wall with intestinal lining epithelium. We report a case of mediastinal enteric duplication cyst with aberrant pancreatic tissue in a neonate due to its rarity and early presentation. A neonate presented with respiratory distress and a cystic mass in the right posterior mediastinum. The lesion was excised and on histopathological analysis the diagnosis of mediastinal enteric duplication cyst was made. Also, aberrant pancreatic tissue which has been reported rarely was noted in this case. We discuss this case and review similar cases reported in literature.
纵隔肠源性重复囊肿是一种罕见的先天性畸形，主要见于新生儿和婴儿。它是前肠重复囊肿家族中的一个独特实体。由于占位效应，它可表现为呼吸窘迫，因此手术切除是首选治疗方法。组织学上，其特征是具有肠内衬上皮的双层平滑肌壁。我们报告一例新生儿纵隔肠源性重复囊肿合并异位胰腺组织的病例，因其罕见性及早期表现。一名新生儿出现呼吸窘迫，右后纵隔有一个囊性肿块。病变被切除，经组织病理学分析诊断为纵隔肠源性重复囊肿。此外，该病例中还发现了罕见报道的异位胰腺组织。我们讨论此病例并回顾文献中报道的类似病例。
