巨大纵隔囊肿内的异位胰腺组织：一种罕见的情况。
Aberrant pancreatic tissue in a giant mediastinal cyst: an uncommon entity.
作者信息
Njem Josiah Miner, Ugwu Benjamin, Collins John, Emmanuel Innocent, Philip Ojile Akpa, Awodi John
机构信息
Cardiothoracic Surgery Unit, Department of Surgery Jos University Teaching Hospital, Jos, Nigeria.
Department of Paediatrics, Jos University Teaching Hospital, Jos, Nigeria.
出版信息
J Cardiothorac Surg. 2019 Jul 8;14(1):134. doi: 10.1186/s13019-019-0955-2.
BACKGROUND
Heterotopia of pancreatic tissue in the thorax and mediastinum is uncommon, although, a common developmental anomaly in the gastrointestinal tract where the aberrant tissue is a component of gastrointestinal duplication cysts, intralobular pulmonary sequestration or teratomas.
CASE PRESENTATION
We report a case of an ectopic pancreas located in a giant mediastinal cyst in a 2-year old girl who presented with severe dyspnoea due to external compression of the intra-thoracic structures, mainly the right main bronchus. Surgical resection was carried out with complete relief of symptoms. The cyst was confirmed histopathologically to contain pancreatic tissue. Literature review showed that this is an uncommon presentation hence the need to report the case.
CONCLUSION
Heterotopia of the pancreas although, an uncommon occurrence in the thorax and mediastinum, should be considered when dealing with cystic lesions of the mediastinum and surgery plays an important role in its management.
TRIAL REGISTRATION
JUTH/DCS/ADM/127/XXV/203. Registered 2nd September 2018.
背景
胰腺组织在胸部和纵隔的异位并不常见，尽管在胃肠道中这是一种常见的发育异常，其中异常组织是胃肠道重复囊肿、小叶内肺隔离症或畸胎瘤的组成部分。
病例报告
我们报告一例位于2岁女童巨大纵隔囊肿内的异位胰腺病例，该女童因胸腔内结构（主要是右主支气管）受压而出现严重呼吸困难。手术切除后症状完全缓解。经组织病理学证实囊肿内含有胰腺组织。文献回顾显示，这种表现并不常见，因此有必要报告该病例。
结论
胰腺异位在胸部和纵隔虽不常见，但在处理纵隔囊性病变时应予以考虑，手术在其治疗中起着重要作用。
试验注册
JUTH/DCS/ADM/127/XXV/203。2018年9月2日注册。
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