成功使用含少量FVIII的高纯度血浆血管性血友病因子浓缩物对重度（3型）血管性血友病进行长期预防。 - Suppr

Successful Use of a Highly Purified Plasma von Willebrand Factor Concentrate Containing Little FVIII for the Long-Term Prophylaxis of Severe (Type 3) von Willebrand's Disease.

作者信息

Simurda Tomas, Dobrotova Miroslava, Skornova Ingrid, Sokol Juraj, Kubisz Peter, Stasko Jan

机构信息

National Centre of Hemostasis and Thrombosis, Department of Hematology and Transfusiology, Comenius University in Bratislava, Jessenius Faculty of Medicine in Martin, Martin, Slovakia.

出版信息

Semin Thromb Hemost. 2017 Sep;43(6):639-641. doi: 10.1055/s-0037-1603362. Epub 2017 Jun 13.

DOI:10.1055/s-0037-1603362

PMID:28609796

Abstract

摘要

相似文献

Successful Use of a Highly Purified Plasma von Willebrand Factor Concentrate Containing Little FVIII for the Long-Term Prophylaxis of Severe (Type 3) von Willebrand's Disease.成功使用含少量FVIII的高纯度血浆血管性血友病因子浓缩物对重度（3型）血管性血友病进行长期预防。

Semin Thromb Hemost. 2017 Sep;43(6):639-641. doi: 10.1055/s-0037-1603362. Epub 2017 Jun 13.

Heterogeneous abnormalities in the multimeric structure, antigenic properties, and plasma-platelet content of factor VIII/von Willebrand factor in subtypes of classic (type I) and variant (type IIA) von Willebrand's disease.经典（I型）和变异型（IIA型）血管性血友病亚型中VIII因子/血管性血友病因子的多聚体结构、抗原特性及血浆-血小板含量的异质性异常

J Lab Clin Med. 1983 Mar;101(3):411-25.

Carbohydrate of the factor VIII/von Willebrand factor in von Willebrand's disease.血管性血友病中因子VIII/血管性血友病因子的碳水化合物

J Clin Invest. 1979 Nov;64(5):1298-302. doi: 10.1172/JCI109585.

Stabilization of factor VIII in plasma by the von Willebrand factor. Studies on posttransfusion and dissociated factor VIII and in patients with von Willebrand's disease.血管性血友病因子对血浆中凝血因子VIII的稳定作用。关于输血后及解离的凝血因子VIII的研究以及血管性血友病患者的研究。

J Clin Invest. 1977 Aug;60(2):390-404. doi: 10.1172/JCI108788.

Hemophilia and von Willebrand's disease: 2. Management. Association of Hemophilia Clinic Directors of Canada.血友病和血管性血友病：2. 管理。加拿大血友病诊所主任协会

CMAJ. 1995 Jul 15;153(2):147-57.

Heightened interaction between platelets and factor VIII/von Willebrand factor in a new subtype of von Willebrand's disease.血管性血友病新亚型中血小板与凝血因子VIII/血管性血友病因子之间的相互作用增强。

N Engl J Med. 1980 May 8;302(19):1047-51. doi: 10.1056/NEJM198005083021902.

Clinical efficacy and safety of the factor VIII/von Willebrand factor concentrate BIOSTATE in patients with von Willebrand's disease: a prospective multi-centre study.VIII 因子/von Willebrand 因子浓缩物 BIOSTATE 在 von Willebrand 病患者中的临床疗效和安全性：一项前瞻性多中心研究。

Haemophilia. 2010 Jul 1;16(4):615-24. doi: 10.1111/j.1365-2516.2010.02206.x. Epub 2010 Mar 16.

Platelet adhesion to collagen in subtypes of type I von Willebrand's disease is dependent on platelet von Willebrand factor.I型血管性血友病各亚型中血小板对胶原蛋白的黏附依赖于血小板血管性血友病因子。

Thromb Haemost. 1990 Oct 22;64(2):227-31.

Variant von Willebrand's disease: characterization of two subtypes by analysis of multimeric composition of factor VIII/von Willebrand factor in plasma and platelets.血管性血友病：通过分析血浆和血小板中因子VIII/血管性血友病因子的多聚体组成来鉴定两种亚型

J Clin Invest. 1980 Jun;65(6):1318-25. doi: 10.1172/JCI109795.

The effects of desmopressin on plasma factor VIII/von Willebrand factor activity in dogs with von Willebrand's disease.去氨加压素对患有血管性血友病的犬血浆凝血因子VIII/血管性血友病因子活性的影响。

Can J Vet Res. 1987 Apr;51(2):189-93.

引用本文的文献

Polyphosphate Activates von Willebrand Factor Interaction with Glycoprotein Ib in the Absence of Factor VIII In Vitro.多聚磷酸盐在体外激活 von Willebrand 因子与糖蛋白 Ib 的相互作用而无需因子 VIII。

Int J Mol Sci. 2022 Nov 15;23(22):14118. doi: 10.3390/ijms232214118.

ADAMTS13, VWF, and Endotoxin Are Interrelated and Associated with the Severity of Liver Cirrhosis via Hypercoagulability.ADAMTS13、血管性血友病因子（VWF）和内毒素相互关联，并通过高凝状态与肝硬化的严重程度相关。

J Clin Med. 2022 Mar 26;11(7):1835. doi: 10.3390/jcm11071835.

Clinical Application of Factor VIII:C to VWF:Ag Ratio for the Screening of Haemophilia A Carriers.因子VIII：C与血管性血友病因子：抗原比值在甲型血友病携带者筛查中的临床应用

J Clin Med. 2022 Mar 18;11(6):1686. doi: 10.3390/jcm11061686.

Impact of Primary Hemostasis Disorders on Late Major Bleeding Events among Anticoagulated Atrial Fibrillation Patients Treated by TAVR.原发性止血障碍对经导管主动脉瓣置换术治疗的抗凝心房颤动患者晚期严重出血事件的影响。

J Clin Med. 2021 Dec 31;11(1):212. doi: 10.3390/jcm11010212.

Multimer Analysis of Von Willebrand Factor in Von Willebrand Disease with a Hydrasys Semi-Automatic Analyzer-Single-Center Experience.使用Hydrasys半自动分析仪对血管性血友病因子进行多聚体分析——单中心经验

Diagnostics (Basel). 2021 Nov 20;11(11):2153. doi: 10.3390/diagnostics11112153.

The Pathophysiology and Management of Hemorrhagic Shock in the Polytrauma Patient.多发伤患者失血性休克的病理生理学与处理

J Clin Med. 2021 Oct 19;10(20):4793. doi: 10.3390/jcm10204793.

The Use of Total Thrombus Formation Analysis System as a Tool to Assess Platelet Function in Bleeding and Thrombosis Risk-A Systematic Review.全血栓形成分析系统在出血和血栓形成风险评估中的应用：系统评价。

Int J Mol Sci. 2021 Aug 10;22(16):8605. doi: 10.3390/ijms22168605.

The Role of the Proteasome in Platelet Function.蛋白酶体在血小板功能中的作用。

Int J Mol Sci. 2021 Apr 13;22(8):3999. doi: 10.3390/ijms22083999.

Spongostan Leads to Increased Regeneration of a Rat Calvarial Critical Size Defect Compared to NanoBone and Actifuse.与纳米骨和活性融合材料相比，海绵骨素可促进大鼠颅骨临界尺寸缺损的再生。

Materials (Basel). 2021 Apr 14;14(8):1961. doi: 10.3390/ma14081961.

VWF, Platelets and the Antiphospholipid Syndrome.血管性血友病因子、血小板与抗磷脂综合征。

Int J Mol Sci. 2021 Apr 18;22(8):4200. doi: 10.3390/ijms22084200.

文献AI研究员

20分钟写一篇综述，助力文献阅读效率提升50倍。

立即体验

用中文搜PubMed

大模型驱动的PubMed中文搜索引擎

马上搜索

文档翻译

学术文献翻译模型，支持多种主流文档格式。

立即体验

Successful Use of a Highly Purified Plasma von Willebrand Factor Concentrate Containing Little FVIII for the Long-Term Prophylaxis of Severe (Type 3) von Willebrand's Disease.

作者信息

机构信息

出版信息

相似文献

引用本文的文献

文献AI研究员

用中文搜PubMed

文档翻译

Suppr 超能文献

相似文献

引用本文的文献