Chung Raymond, Chawla Ashish, Peh Wilfred Cg
Department of Diagnostic Radiology, Khoo Teck Puat Hospital, Singapore.
Singapore Med J. 2017 Jun;58(6):289-293. doi: 10.11622/smedj.2017049.
Wünderlich syndrome is a rare entity characterised by spontaneous retroperitoneal haemorrhage with renal origin. We present a case of Wünderlich syndrome secondary to clotting dyscrasia in a 64-year-old woman. The patient experienced a second Wünderlich haemorrhagic event with metachronous pseudoaneurysm formation, which was likely secondary to the large subcapsular haematoma stripping the renal capsule and tearing the cortical arteries. Selective pseudoaneurysm embolisations were successfully performed on both occasions. This clinical entity, its imaging differential diagnoses and management are discussed.
温德利希综合征是一种罕见的病症,其特征为源于肾脏的自发性腹膜后出血。我们报告一例64岁女性因凝血功能障碍继发温德利希综合征的病例。该患者经历了第二次温德利希出血事件,并出现了异时性假性动脉瘤形成,这可能是由于巨大的肾包膜下血肿剥脱肾包膜并撕裂皮质动脉所致。两次均成功进行了选择性假性动脉瘤栓塞术。本文讨论了这一临床实体、其影像学鉴别诊断及治疗方法。