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多发性大动脉炎和家族性高胆固醇血症患者左心功能障碍的多模态评估。

Multimodality assessment of left ventricular dysfunction in Takayasu arteritis and familial hypercholesterolaemia.

机构信息

Department of Cardiovascular Medicine, National Cerebral and Cardiovascular Center, Suita, 565-8565, Osaka, Japan.

Department of Molecular Innovation in Lipidology, National Cerebral and Cardiovascular Center, Suita, 565-8565, Osaka, Japan.

出版信息

ESC Heart Fail. 2017 Nov;4(4):655-659. doi: 10.1002/ehf2.12196. Epub 2017 Jul 31.

Abstract

Although left ventricular (LV) systolic dysfunction in patients suffering from Takayasu arteritis (TA) has been reported, little is known regarding the development of heart failure in these patients. We report a novel finding of active TA and familial hypercholesterolaemia presenting with severe LV dysfunction through multimodality assessments of LV systolic dysfunction.

摘要

虽然已有研究报道了患有 Takayasu 动脉炎(TA)的患者存在左心室(LV)收缩功能障碍,但对于这些患者发生心力衰竭的情况知之甚少。我们报告了一例新的活动性 TA 和家族性高胆固醇血症病例,通过 LV 收缩功能障碍的多模式评估发现存在严重的 LV 功能障碍。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f953/5695181/3158cd8f4769/EHF2-4-655-g001.jpg

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