Kanitkar M, JOSHi S N, Roy N Dutta
Graded Specialist Paediatrics, Military Hospital, Jhansi. 284 001.
Classified Socialist Paediatrics, Military Hospital, Jhansi. 284 001.
Med J Armed Forces India. 1994 Jan;50(1):63-65. doi: 10.1016/S0377-1237(17)31042-0. Epub 2017 Jun 27.
Two cases of Wilson's disease are reported. First case presented with fulminant hepatic failure and had a fatal outcome. The second had an insiduous onset, neurological manifestations, and is progressing satisfactorily on zinc therapy. Problems in diagnosis and treatment are highlighted.
报告了两例威尔逊氏病。第一例表现为暴发性肝衰竭,最终死亡。第二例起病隐匿,有神经学表现,目前接受锌治疗,病情进展良好。文中强调了诊断和治疗方面的问题。