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儿童颅骨筋膜炎(CFC):一种罕见疾病的不寻常临床病例。

Cranial fasciitis of childhood (CFC): an unusual clinical case of a rare disease.

作者信息

Zavras Niki, Poddighe Dimitri

机构信息

Department of Pediatrics, Università degli Studi di Pavia, Pavia, Lombardia, Italy.

Department of Pediatrics, ASST Melegnano e Martesana, Vizzolo Predabissi, Italy.

出版信息

BMJ Case Rep. 2017 Sep 13;2017:bcr-2017-220859. doi: 10.1136/bcr-2017-220859.

DOI:10.1136/bcr-2017-220859
PMID:28903973
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5623234/
Abstract

Cranial fasciitis of childhood (CFC) is a very uncommon tumour of the scalp, which is almost exclusively observed in the first years of life. It is a benign proliferation of fibroblasts, but its rapid growth rate may resemble a malignant disease. This disease may be suspected from clinical and radiological features, but a definitive diagnosis may be achieved only by pathological examination. We report a case whose onset was in late childhood and whose clinical and radiological characteristics were atypical.

摘要

儿童颅骨筋膜炎(CFC)是一种非常罕见的头皮肿瘤,几乎仅在生命的最初几年出现。它是成纤维细胞的良性增生,但其快速生长速度可能类似于恶性疾病。根据临床和放射学特征可能怀疑此病,但只有通过病理检查才能做出明确诊断。我们报告一例发病于儿童晚期且临床和放射学特征不典型的病例。

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BMJ Case Rep. 2017 Sep 13;2017:bcr-2017-220859. doi: 10.1136/bcr-2017-220859.
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本文引用的文献

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Infantile cranial fasciitis: case-based review and operative technique.婴儿颅骨筋膜炎:基于病例的综述及手术技术
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Cranial fasciitis presenting as a frontonasal mass.表现为额鼻肿物的颅骨筋膜炎。
J Craniofac Surg. 2009 Jul;20(4):1197-9. doi: 10.1097/SCS.0b013e3181acdc98.
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Cranial fasciitis of childhood.儿童颅骨筋膜炎
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Cranial fasciitis of childhood.儿童颅骨筋膜炎
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