Department of Radiology, Hunan Children's Hospital, University of South China, No. 86 Ziyuan Road, Changsha, Hunan, 410007, China.
Department of Pathology, Hunan Children's Hospital, University of South China, Changsha, China.
BMC Pediatr. 2022 Sep 17;22(1):551. doi: 10.1186/s12887-022-03610-w.
Cranial fasciitis (CF) is a rare benign fibroproliferative lesion of the skull. To date, the summarized radiologic characteristics and the subtype of the disease have not been reported. our purpose was to summarize the characteristic clinicoradiology features and management of CF and to improve the knowledge of radiologists and clinicians.
We searched our institution's database and retrieved the clinical and radiologic data of CF patients confirmed by histopathological examination. The clinicoradiology features and management of CF were analysed retrospectively.
A total of 14 CF patients were included. A total of 85.7% of the patients presented with a painless, firm, nonmobile and single mass. Tenderness and multiple masses were found in 14.3% of the patients. The mass was clearly increased in 2 patients and gradually increased in 5 patients in the short term. We divided these patients into three types based on the CT characteristics. The characteristic features of type I (9 patients) presented as an expansive and osteolytic bone destruction with a soft tissue mass. Type II (2 patients) presented as a scalp mass with mild erosion of the outer skull plate. Type III (3 patients) presented as a scalp mass without skull destruction. All patients underwent surgical resection. For type I patients, craniectomy and cranioplasty were performed. For type II patients, complete excision of the scalp mass with local skull curettage was performed. For type III patients, complete excision of the scalp mass was performed. There were no cases of recurrence after follow-up.
CF usually presents as a painless, firm, nonmobile and single mass with a clear boundary. There are generally three types of MSCT findings: bone destruction with a soft tissue mass, a scalp mass with erosion of the skull and a scalp mass. Different management strategies should be utilized for the various types of CF.
颅筋膜纤维织炎（CF）是一种罕见的颅骨良性纤维增生性病变。迄今为止，尚未有该病的总结性影像学特征和亚型报道。我们的目的是总结 CF 的特征性临床影像学特征和处理方法，以提高放射科医生和临床医生的认识。
我们检索了本机构的数据库，并检索了经组织病理学检查证实的 CF 患者的临床和影像学数据。回顾性分析 CF 的临床影像学特征和处理方法。
共纳入 14 例 CF 患者。85.7%的患者表现为无痛、坚硬、不可移动且单发的肿块。14.3%的患者存在压痛和多个肿块。2 例患者肿块明显增大，5 例患者短期内肿块逐渐增大。根据 CT 特征，我们将这些患者分为 3 型。I 型（9 例）的特征表现为膨胀性和溶骨性骨破坏伴软组织肿块。II 型（2 例）表现为头皮肿块，颅骨外板轻度侵蚀。III 型（3 例）表现为头皮肿块，无颅骨破坏。所有患者均行手术切除。I 型患者行颅骨切除术和颅骨成形术。II 型患者行头皮肿块完整切除及局部颅骨刮除术。III 型患者行头皮肿块完整切除术。随访后均无复发。
CF 通常表现为无痛、坚硬、不可移动且单发的肿块，边界清晰。MSCT 通常有 3 种表现：骨破坏伴软组织肿块、颅骨侵蚀伴头皮肿块、头皮肿块。对于不同类型的 CF，应采用不同的处理策略。
