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一例罕见的伴有广泛坏死的E型淋巴瘤样丘疹病。

An unusual case of lymphomatoid papulosis type E with extensive necrosis.

作者信息

Pindado-Ortega Cristina, Fonda-Pascual Pablo, Buendía-Castaño Diego, Fernández-González Pablo, Peña-Jaimes Lourdes, Carrillo-Gijón Rosario

机构信息

Department of Dermatology, Hospital Ramon Y Cajal, Madrid, Spain.

Department of Pathology, Hospital Ramon Y Cajal, Madrid, Spain.

出版信息

Indian J Dermatol Venereol Leprol. 2018 Jul-Aug;84(4):515-517. doi: 10.4103/ijdvl.IJDVL_871_16.

DOI:10.4103/ijdvl.IJDVL_871_16
PMID:29067932
Abstract

Lymphomatoid papulosis type E (LyP) is a recently described subtype of LyP characterized by an angioinvasive infiltrate of atypical lymphocytes expressing CD30. We present a case of type E LyP with extensive cutaneous necrosis in the histopathological evaluation which was misdiagnosed as an ulcerative form of bacterial skin infection. The remarkable cutaneous necrosis showed in our case might be related to the angiodestructive infiltrate that was present in this circumstance.

摘要

E型淋巴瘤样丘疹病(LyP)是最近描述的LyP亚型,其特征为表达CD30的非典型淋巴细胞的血管浸润性浸润。我们报告一例E型LyP,在组织病理学评估中出现广泛皮肤坏死,最初被误诊为细菌性皮肤感染的溃疡性形式。我们病例中出现的显著皮肤坏死可能与这种情况下存在的血管破坏性浸润有关。

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Histologic and Immunohistochemical Patterns in Lymphomatoid Papulosis: A Systematic Review of Published Cases.淋巴瘤样丘疹病的组织学和免疫组化模式:已发表病例的系统评价
Dermatopathology (Basel). 2025 Feb 12;12(1):6. doi: 10.3390/dermatopathology12010006.
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Lymphomatoid papulosis type E: An indolent diagnosis in disguise.
J Dermatol. 2025 Mar;52(3):e210-e211. doi: 10.1111/1346-8138.17642. Epub 2025 Jan 20.