Kawata Takahito, Tada Kohei, Kobayashi Masayuki, Sakamoto Takashi, Takiuchi Yoko, Iwai Fumie, Sakurada Maki, Hishizawa Masakatsu, Shirakawa Kotaro, Shindo Keisuke, Sato Hironori, Takaori-Kondo Akifumi
Department of Hematology and Oncology, Graduate School of Medicine, Kyoto University, Kyoto, Japan.
Pathogen Genomics Center, National Institute of Infectious Diseases, Tokyo, Japan.
Cancer Sci. 2018 Jan;109(1):103-111. doi: 10.1111/cas.13431. Epub 2017 Nov 22.
Adult T-cell leukemia (ATL) has a poor prognosis as a result of severe immunosuppression and rapid tumor progression with resistance to conventional chemotherapy. Recent integrated-genome analysis has revealed mutations in many genes involved in the T-cell signaling pathway, suggesting that the aberration of this pathway is an important factor in ATL pathogenesis and ATL-cell proliferation. We screened a siRNA library to examine signaling-pathway functionality and found that the PI3K/Akt/mTOR pathway is critical to ATL-cell proliferation. We therefore investigated the effect of mammalian target of rapamycin (mTOR) inhibitors, including the dual inhibitors PP242 and AZD8055 and the mTORC1 inhibitors rapamycin and everolimus, on human T-cell leukemia virus type 1 (HTLV-1)-infected-cell and ATL-cell lines. Both dual inhibitors inhibited the proliferation of all tested cell lines by inducing G1-phase cell-cycle arrest and subsequent cell apoptosis, whereas the effects of the 2 mTORC1 inhibitors were limited, as they did not induce cell apoptosis. In the ATL-cell lines and in the primary ATL samples, both dual inhibitors inhibited phosphorylation of AKT at serine-473, a target of mTORC2, as well as that of S6K, whereas the mTORC1 inhibitors only inhibited mTORC1. Furthermore, AZD8055 more significantly inhibited the in vivo growth of the ATL-cell xenografts than did everolimus. These results indicate that the PI3K/mTOR pathway is critical to ATL-cell proliferation and might thus be a new therapeutic target in ATL.
成人T细胞白血病(ATL)预后较差,原因是严重免疫抑制以及肿瘤进展迅速且对传统化疗耐药。最近的全基因组分析揭示了许多参与T细胞信号通路的基因突变,这表明该通路的异常是ATL发病机制和ATL细胞增殖的重要因素。我们筛选了一个小干扰RNA文库来检测信号通路功能,发现PI3K/Akt/mTOR通路对ATL细胞增殖至关重要。因此,我们研究了雷帕霉素哺乳动物靶点(mTOR)抑制剂,包括双重抑制剂PP242和AZD8055以及mTORC1抑制剂雷帕霉素和依维莫司,对1型人类T细胞白血病病毒(HTLV-1)感染细胞和ATL细胞系的影响。两种双重抑制剂均通过诱导G1期细胞周期停滞和随后的细胞凋亡来抑制所有测试细胞系的增殖,而两种mTORC1抑制剂的作用有限,因为它们未诱导细胞凋亡。在ATL细胞系和原发性ATL样本中,两种双重抑制剂均抑制了mTORC2的靶点丝氨酸473处的AKT磷酸化以及S6K的磷酸化,而mTORC1抑制剂仅抑制mTORC1。此外,与依维莫司相比,AZD8055更显著地抑制了ATL细胞异种移植物的体内生长。这些结果表明,PI3K/mTOR通路对ATL细胞增殖至关重要,因此可能是ATL的一个新治疗靶点。