一名青春期女孩的外阴原始神经外胚层肿瘤

Narayanan Geetha, Rajan Varun, Puthusseri Jaisankar, Kattoor Jayasree, Soman Lali V

Department of Medical Oncology, Regional Cancer Centre, Trivandrum 695011, India.

Department of Pathology, Regional Cancer Centre, Trivandrum 695011, India.

World J Oncol. 2014 Dec;5(5-6):220-222. doi: 10.14740/wjon819w. Epub 2014 Dec 3.

Extraskeletal primitive neuroectodermal tumor (PNET) is rare and that affecting the female genital tract is extremely rare. We report the case of a 17-year-old girl who presented with swelling of the clitorus. She underwent excision and histopathology was PNET. She received chemotherapy and radiation and achieved complete remission. However, she relapsed locally and systemically soon, progressed and died.

骨外原始神经外胚层肿瘤（PNET）罕见，而累及女性生殖道的情况极为罕见。我们报告一例17岁女性病例，其表现为阴蒂肿胀。她接受了切除术，组织病理学检查结果为PNET。她接受了化疗和放疗并实现完全缓解。然而，她很快出现局部和全身复发，病情进展并死亡。