Chen Ji, Sun Mengjiao, Sun Bin, Yi Jun, Jiang Bin, Huang Lei
Department of General Surgery, Children's Hospital of Nanjing Medical University, Nanjing, 210008, China.
Department of Hematology/Oncology, Children's Hospital of Nanjing Medical University, Nanjing, China.
J Med Case Rep. 2017 Nov 21;11(1):327. doi: 10.1186/s13256-017-1488-8.
Almost all hepatoblastomas are isolated to the liver. Hepatoblastoma arising from and limited to extrahepatic tissue is an extremely rare clinical entity.
Here we present a case of a 7-year-old Chinese boy of Han ethnicity with hepatoblastoma originating from the hepatogastric ligament. A complete resection was performed and the entire course was uneventful. He received six cycles of postoperative chemotherapy and had no signs of recurrence for 3 years after surgery.
Hepatoblastoma arising from extrahepatic tissue is extremely rare. A pedunculated hepatoblastoma is prone to hemorrhage and tumor metastasis. The best treatment for a long-term cure is complete resection of the primary tumor combined with chemotherapy.
几乎所有肝母细胞瘤都局限于肝脏。起源于肝外组织并局限于该部位的肝母细胞瘤是一种极其罕见的临床病症。
在此，我们报告一例7岁汉族中国男孩，其肝母细胞瘤起源于肝胃韧带。进行了完整切除，整个过程顺利。他接受了六个周期的术后化疗，术后3年无复发迹象。
起源于肝外组织的肝母细胞瘤极为罕见。带蒂肝母细胞瘤易于出血和发生肿瘤转移。实现长期治愈的最佳治疗方法是完整切除原发肿瘤并联合化疗。
