Gunawan Hendra, Haryati Nia Srie, Suwarsa Oki
Department of Dermatology and Venereology, Faculty of Medicine, Universitas Padjadjaran - Dr. Hasan Sadikin Hospital, Bandung, Indonesia.
Case Rep Dermatol. 2017 Nov 14;9(3):231-235. doi: 10.1159/000484037. eCollection 2017 Sep-Dec.
Swan neck deformity is a hyperextension of the proximal interphalangeal (PIP) joints and flexion of the distal interphalangeal (DIP) joints. Claw hand is a hyperextension of the metacarpal joints and flexion of the PIP joints, accompanied by reduced motor strength. A 23-year-old female, who was released from leprosy treatment, presented with a bend of the second to fifth fingers of both hands. There was hyperextension of the PIP joints and flexion of the DIP joints from the second to fifth fingers of both hands, thickening of the ulnar nerves, and hypoesthesia without motor impairment of the fourth and fifth fingers of both hands. Radiograph examination revealed cupping of the base of the proximal phalangeal joints of the second, third, and fifth fingers of the left hand and of the second and fifth fingers of the right hand. Additionally, narrowing of the metacarpophalangeal joints of the second, third, and fifth fingers of the right hand and sclerosis of the second and fifth fingers of the right hand were also observed. Claw hand is frequently reported in leprosy, while swan neck deformity is frequently reported in rheumatoid arthritis. To our knowledge, this is the first reported case with swan neck deformity caused by arthritis in leprosy.
鹅颈畸形是近端指间关节(PIP)过伸,远端指间关节(DIP)屈曲。爪形手是掌指关节过伸,近端指间关节屈曲,同时伴有肌力减弱。一名23岁已停止麻风病治疗的女性,双手示指至小指出现弯曲。双手示指至小指近端指间关节过伸,远端指间关节屈曲,尺神经增粗,双手第四、五指感觉减退但无运动障碍。X线检查显示左手示指、中指、小指及右手示指、小指近端指骨基底部呈杯状。此外,还观察到右手示指、中指、小指掌指关节变窄,右手示指、小指骨质硬化。爪形手在麻风病中较为常见,而鹅颈畸形在类风湿关节炎中较为常见。据我们所知,这是首例报道的麻风病关节炎导致鹅颈畸形的病例。