板层状鱼鳞病伴严重睑外翻采用口服阿维A进行药物治疗。

Severe ectropion in lamellar ichthyosis managed medically with oral acitretin.

作者信息

Singh Manpreet, Kaur Manpreet, Kaur Ripanjeet, Singh Shakeen

机构信息

Department of Ophthalmology, Post Graduate Institute of Medical Education and Research, Chandigarh, India.

Department of Ophthalmology, Sri Guru Ram Das Institute of Medical Sciences and Research, Amritsar, India.

出版信息

Pediatr Dermatol. 2018 Mar;35(2):e117-e120. doi: 10.1111/pde.13410. Epub 2018 Jan 15.

DOI:10.1111/pde.13410

PMID:29334142

Abstract

Congenital ectropion is commonly associated with lamellar ichthyosis. Severe eyelid ectropion may cause corneal exposure, keratopathy, and permanent corneal scarring. We report a neonate with severe, bilateral, congenital ectropion and eclabium managed using oral retinoids. Both corneas were protected with topical antibiotics and lubricating eyedrops and eye ointments. At 12-month follow-up, the child was doing well, with no ectropion or corneal opacity.

摘要

先天性睑外翻通常与板层状鱼鳞病相关。严重的眼睑外翻可能导致角膜暴露、角膜病变和永久性角膜瘢痕形成。我们报告一例使用口服维甲酸治疗的患有严重双侧先天性睑外翻和唇外翻的新生儿。双眼角膜均使用局部抗生素以及润滑眼药水和眼膏进行保护。在12个月的随访中，患儿情况良好，无睑外翻或角膜混浊。