特发性肥厚性硬脑膜炎作为颈髓压迫症的罕见病因。
Idiopathic hypertrophic pachymeningitis as a rare cause of cervical compressive myelopathy.
作者信息
Fukuda Aya, Punaro Elizabete, Rogério Fábio, de Souza Queiroz Luciano, Reis Fabiano
机构信息
Department of Radiology, State University of Campinas, State University of Campinas, SP, Brazil.
Department of Pathology, State University of Campinas, State University of Campinas, SP, Brazil.
出版信息
J Craniovertebr Junction Spine. 2017 Oct-Dec;8(4):387-389. doi: 10.4103/jcvjs.JCVJS_118_17.
The spinal form of idiopathic hypertrophic pachymeningitis (IHP) is a rare condition characterized by a chronic progressive diffuse inflammatory fibrosis of the dura mater, which may evolve to the compression of the spinal cord. We present a case report about IHP focusing on its features in magnetic resonance imaging, which are determined by an intradural extramedullary mass in the cervical spine showing hypointensity on T2-weighted images and peripheral enhancement, causing compression of the spinal cord. Histological analysis showed a nonspecific chronic inflammatory process in dense fibrous tissue. The patient had a good outcome after therapy with steroids.
特发性肥厚性硬脑膜炎（IHP）的脊髓型是一种罕见疾病，其特征为硬脑膜的慢性进行性弥漫性炎性纤维化，可能会发展为脊髓受压。我们呈现一份关于IHP的病例报告，重点关注其磁共振成像特征，这些特征由颈椎硬膜内髓外肿块决定，该肿块在T2加权图像上呈低信号且周边强化，导致脊髓受压。组织学分析显示致密纤维组织中有非特异性慢性炎症过程。该患者经类固醇治疗后预后良好。
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