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特发性肥厚性硬脊膜脑膜炎:两例典型磁共振成像表现的病例报告。

Idiopathic hypertrophic spinal pachymeningitis: report of two cases with typical MR imaging findings.

作者信息

Pai S, Welsh C T, Patel S, Rumboldt Z

机构信息

Department of Neurosurgery, Medical University of South Carolina, Charleston, SC 29425, USA.

出版信息

AJNR Am J Neuroradiol. 2007 Mar;28(3):590-2.

PMID:17353343
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7977824/
Abstract

Two patients with a chronic progressive myelopathy were successfully surgically treated and idiopathic hypertrophic spinal pachymeningitis (IHSP) was found on histology. In both patients, an extensive extramedullary mass of low T2 signal with peripheral contrast enhancement was compressing the spinal cord on MR imaging. This imaging appearance in patients with chronic progressive myelopathy should suggest the diagnosis of IHSP.

摘要

两名患有慢性进行性脊髓病的患者接受了成功的手术治疗,组织学检查发现为特发性肥厚性硬脊膜脑膜炎(IHSP)。在这两名患者中,磁共振成像(MR)显示一个广泛的髓外肿块,T2信号低,周边有对比增强,压迫脊髓。慢性进行性脊髓病患者的这种影像学表现应提示IHSP的诊断。

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Idiopathic hypertrophic cranial pachymeningitis masquerading as Tolosa-Hunt syndrome.伪装成托洛萨-亨特综合征的特发性肥厚性硬脑膜炎。
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