Voldsgaard P, Kryger-Baggesen N, Lisse I
Department of Paediatrics, University of Copenhagen, Hvidovre Hospital, Denmark.
Acta Paediatr. 1994 Jul;83(7):791-3. doi: 10.1111/j.1651-2227.1994.tb13144.x.
Complete agenesis of pancreas is a rare and lethal condition. Four cases have previously been reported in combination with other malformations, such as severe intrauterine growth retardation, hyperglycaemia and meconium ileus. We report a case of pancreatic agenesis as a single anomaly. The child died when 48 h old with severe metabolic acidosis. The literature is surveyed and the pathogenesis is discussed.