梗阻性半阴道并同侧肾异常（OHVIRA）综合征
Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome.
作者信息
Al Ghafri Aziza, Fida Alaeddin, Al-Gharras Abdulaziz
机构信息
Radiology Department, Ibri Regional Hospital, Al Dhahira, Oman.
Radiology Department, King Faisal Specialist Hospital and Research Centre, Riyadh, Saudi Arabia.
出版信息
Oman Med J. 2018 Jan;33(1):69-71. doi: 10.5001/omj.2018.13.
Abstract
Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare congenital abnormality of the female urogenital tract. We reported OHVIRA syndrome in a 15-year-old girl, who was referred to King Faisal Specialist Hospital and Research Centre, due to hematocolpos and an imperforate hymen. The patient was diagnosed as having an absent right kidney since childhood. She presented with progressive development of lower abdominal discomfort and an abdominopelvic mass. She had no history of urinary complaints. Here, we describe our findings from the abdominal ultrasound and magnetic resonance imaging.
摘要
梗阻性半阴道与同侧肾异常（OHVIRA）综合征是一种罕见的女性泌尿生殖道先天性异常。我们报告了一名15岁女孩的OHVIRA综合征，她因阴道积血和处女膜闭锁被转诊至法赫德国王专科医院和研究中心。该患者自幼被诊断为右肾缺如。她出现了下腹部不适和腹盆腔肿块的进行性发展。她没有泌尿系统症状的病史。在此，我们描述腹部超声和磁共振成像的检查结果。
相似文献
1
Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome.
Oman Med J. 2018 Jan;33(1):69-71. doi: 10.5001/omj.2018.13.
2
Right-sided obstructed hemivagina ipsilateral renal agenesis (OHVIRA): A case report.
Case Rep Womens Health. 2020 Mar 3;26:e00185. doi: 10.1016/j.crwh.2020.e00185. eCollection 2020 Apr.
3
Uterine didelphys associated with obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome.
Radiol Case Rep. 2015 Nov 6;5(1):327. doi: 10.2484/rcr.v5i1.327. eCollection 2010.
4
Unusual case of OHVIRA syndrome with a single uterus, unrecognized before labor and followed by an intrapartal rupture of obstructed hemivagina.
Arch Gynecol Obstet. 2014 Nov;290(5):855-8. doi: 10.1007/s00404-014-3339-9. Epub 2014 Jul 17.
5
OHVIRA syndrome: Early recognition prevents genitourinary complications.
Ultrasound. 2023 Feb;31(1):61-64. doi: 10.1177/1742271X221102576. Epub 2022 Jun 20.
6
Wolffian Origin of Vagina Unfolds the Embryopathogenesis of OHVIRA (Obstructed Hemivagina and Ipsilateral Renal Anomaly) Syndrome and Places OHVIRA as a Female Counterpart of Zinner Syndrome in Males.
Pol J Radiol. 2016 Nov 19;81:549-556. doi: 10.12659/PJR.898244. eCollection 2016.
7
Obstructed hemivagina and ipsilateral renal anomaly syndrome in an association with endometriosis: Role of Magnetic Resonance Imaging in diagnosis.
Med J Malaysia. 2024 Aug;79(Suppl 4):83-86.
8
Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) - A Fetal Autopsy Case.
J Pediatr Adolesc Gynecol. 2022 Oct;35(5):593-596. doi: 10.1016/j.jpag.2022.02.003. Epub 2022 Mar 8.
9
OHVIRA-syndrome (Obstructed hemivagina with ipsilateral renal anomaly) as differential diagnosis of acute lower abdominal pain.
Ann Ital Chir. 2023 Mar 20;12:S2239253X23038720.
10
OHVIRA syndrome (obstructed hemivagina and ipsilateral renal anomaly) with uterus didelphys, an unusual presentation.
J Pediatr Adolesc Gynecol. 2012 Apr;25(2):e23-e25. doi: 10.1016/j.jpag.2011.11.004.
引用本文的文献
1
Diagnosis of congenital oblique vaginal septum syndrome: A case report and literature review.
Int J Surg Case Rep. 2024 Nov;124:110451. doi: 10.1016/j.ijscr.2024.110451. Epub 2024 Oct 15.
2
Multimodality imaging of acute gynecological emergencies-a pictorial essay.
Abdom Radiol (NY). 2024 Nov;49(11):4042-4056. doi: 10.1007/s00261-024-04399-1. Epub 2024 Jun 5.
3
A rare case of obstructed hemivagina with uterus didelphys and ipsilateral renal anomaly syndrome.
SAGE Open Med Case Rep. 2024 May 22;12:2050313X241256517. doi: 10.1177/2050313X241256517. eCollection 2024.
4
Herlyn-Werner-Wunderlich syndrome: Challenges in diagnosis and management.
Narra J. 2023 Aug;3(2):e223. doi: 10.52225/narra.v3i2.223. Epub 2023 Aug 28.
5
Challenges in Diagnosing Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome: Case Report of a Rare Condition.
J Hum Reprod Sci. 2023 Jul-Sep;16(3):257-259. doi: 10.4103/jhrs.jhrs_26_23. Epub 2023 Sep 29.
6
Herlyn-Werner-Wunderlich syndrome also known as obstructed hemivagina and ipsilateral renal anomaly: A case report and a comprehensive review of literature.
Radiol Case Rep. 2023 Jun 6;18(8):2771-2784. doi: 10.1016/j.radcr.2023.05.024. eCollection 2023 Aug.
7
Usefulness of Endoscopy for Female Genital Plastic Surgery: A Series of 4 Cases with Genital Malformations.
Am J Case Rep. 2021 Nov 7;22:e934363. doi: 10.12659/AJCR.934363.
8
A Rare Case of Massive Hematometra with a Tubo-ovarian Abscess in a 16-year-old Female.
Cureus. 2019 Jun 6;11(6):e4845. doi: 10.7759/cureus.4845.
9
Virginity-sparing management of hematocolpos with imperforate hymen: case report and literature review.
SAGE Open Med Case Rep. 2019 May 2;7:2050313X19846765. doi: 10.1177/2050313X19846765. eCollection 2019.
本文引用的文献
1
Single ectopic ureter: diagnostic value of contrast vaginography.
Urology. 2009 Aug;74(2):314-7. doi: 10.1016/j.urology.2009.02.067. Epub 2009 May 24.
2
A tumor of an ectopic ureter mimicking uterine cervix adenocarcinoma: case report and brief review.
Int Urogynecol J Pelvic Floor Dysfunct. 2009 Nov;20(11):1393-5. doi: 10.1007/s00192-009-0893-y. Epub 2009 Apr 29.
3
Complete septate uterus, obstructed hemivagina, and ipsilateral renal anomaly: pregnancy course complicated by a rare urogenital anomaly.
Arch Gynecol Obstet. 2009 Sep;280(3):449-52. doi: 10.1007/s00404-008-0919-6. Epub 2009 Jan 9.
4
Integrated imaging studies and endoscopic management of purulent vaginal discharge in a 6-year-old: vaginal ectopic ureter associated with ipsilateral dysplastic kidney.
Eur J Obstet Gynecol Reprod Biol. 2009 Feb;142(2):160-1. doi: 10.1016/j.ejogrb.2008.10.004. Epub 2008 Nov 25.
5
Herlyn-Werner-Wunderlich syndrome: uterus didelphys, blind hemivagina and ipsilateral renal agenesis. Sonographic and MR findings in 11 cases.
Pediatr Radiol. 2007 Jul;37(7):657-65. doi: 10.1007/s00247-007-0497-y. Epub 2007 May 15.
6
Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome: management and follow-up.
Fertil Steril. 2007 Apr;87(4):918-22. doi: 10.1016/j.fertnstert.2006.11.015. Epub 2007 Feb 22.
7
Ectopic vaginal insertion of an obstructed duplicated ureter in an adult female: demonstration by magnetic resonance imaging.
Clin Imaging. 2007 Jan-Feb;31(1):54-6. doi: 10.1016/j.clinimag.2006.07.001.
8
Single vaginal ectopic ureter of fetal metanephric duct origin, ipsilateral kidney agenesis, and ipsilateral rudimentary uterine horn of the bicornuate uterus.
Gynecol Oncol. 2005 Apr;97(1):276-8. doi: 10.1016/j.ygyno.2004.12.012.
9
Didelphic uterus and obstructed hemivagina with renal agenesis: case report and review of the literature.
J Pediatr Adolesc Gynecol. 2004 Apr;17(2):137-41. doi: 10.1016/j.jpag.2004.01.016.
10
Uterus didelphys associated with obstructed hemivagina and ipsilateral renal agenesis: MR findings in seven cases.
Abdom Imaging. 1998 Jul-Aug;23(4):437-41. doi: 10.1007/s002619900375.
Zotero 插件