梗阻性半阴道并同侧肾异常（OHVIRA）综合征
Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome.
作者信息
Al Ghafri Aziza, Fida Alaeddin, Al-Gharras Abdulaziz
机构信息
Radiology Department, Ibri Regional Hospital, Al Dhahira, Oman.
Radiology Department, King Faisal Specialist Hospital and Research Centre, Riyadh, Saudi Arabia.
出版信息
Oman Med J. 2018 Jan;33(1):69-71. doi: 10.5001/omj.2018.13.
Abstract
Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare congenital abnormality of the female urogenital tract. We reported OHVIRA syndrome in a 15-year-old girl, who was referred to King Faisal Specialist Hospital and Research Centre, due to hematocolpos and an imperforate hymen. The patient was diagnosed as having an absent right kidney since childhood. She presented with progressive development of lower abdominal discomfort and an abdominopelvic mass. She had no history of urinary complaints. Here, we describe our findings from the abdominal ultrasound and magnetic resonance imaging.
摘要
梗阻性半阴道与同侧肾异常（OHVIRA）综合征是一种罕见的女性泌尿生殖道先天性异常。我们报告了一名15岁女孩的OHVIRA综合征，她因阴道积血和处女膜闭锁被转诊至法赫德国王专科医院和研究中心。该患者自幼被诊断为右肾缺如。她出现了下腹部不适和腹盆腔肿块的进行性发展。她没有泌尿系统症状的病史。在此，我们描述腹部超声和磁共振成像的检查结果。
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