AlBaik Taha Mahmoud, Ibrahim Ahmed Tayseer, AbuKaresh Nasim Afif, Anini Ezat Mohammed, Hattab Laith Mohannad, Albandak Maram
Palestine Polytechnic University, Hebron, Palestine.
SAGE Open Med Case Rep. 2024 May 22;12:2050313X241256517. doi: 10.1177/2050313X241256517. eCollection 2024.
Obstructed hemivagina and ipsilateral renal anomaly syndrome, also known as Herlyn-Werner-Wunderlich syndrome, represents a rare congenital anomaly characterized by the presence of an obstructed hemivagina with uterus didelphys and concomitant ipsilateral renal abnormalities. Typically, the clinical presentation includes cyclical abdominal pain, vaginal discharge, and/or a vaginal mass occurring post-menarche. Accurate diagnosis requires a high index of suspicion among clinicians, coupled with a comprehensive understanding of the distinctive features associated with this anomaly. Herein, we present the case of a 13-year-old female patient who complained of persistent lower abdominal pain. Magnetic resonance imaging confirmed the diagnosis of obstructed hemivagina and ipsilateral renal anomaly syndrome, and the patient was successfully treated with a laparotomy involving blood aspiration and hysterectomy. This case report highlights the significance of clinical awareness, prompt diagnosis, and timely therapeutic interventions to mitigate the adverse effects and optimize outcomes in individuals affected by obstructed hemivagina and ipsilateral renal anomaly syndrome.
梗阻性半阴道和同侧肾异常综合征，也称为赫林-韦纳-温德利希综合征，是一种罕见的先天性异常，其特征是存在梗阻性半阴道伴双子宫，同时伴有同侧肾脏异常。通常，临床表现包括月经初潮后出现周期性腹痛、阴道分泌物和/或阴道肿块。准确诊断需要临床医生高度怀疑，并全面了解与这种异常相关的独特特征。在此，我们报告一例13岁女性患者，她主诉持续下腹痛。磁共振成像证实了梗阻性半阴道和同侧肾异常综合征的诊断，患者通过剖腹手术成功治疗，包括抽血和子宫切除术。本病例报告强调了临床意识、及时诊断和及时治疗干预的重要性，以减轻受梗阻性半阴道和同侧肾异常综合征影响的个体的不良影响并优化治疗结果。
