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支气管扩张症的最新进展。

Bronchiectasis update.

机构信息

Division of Pulmonary Critical Care and Sleep Medicine, Georgetown University Medical Center, Washington, District of Columbia, USA.

出版信息

Curr Opin Infect Dis. 2018 Apr;31(2):194-198. doi: 10.1097/QCO.0000000000000445.

DOI:10.1097/QCO.0000000000000445
PMID:29489526
Abstract

PURPOSE OF REVIEW

Bronchiectasis, once thought to be an orphan disease, is being diagnosed with increased frequency in the United States and around the world. The present review aims to provide an update on recent publications on the diagnosis and management of bronchiectasis.

RECENT FINDINGS

Two large bronchiectasis patient registries have published initial reports regarding demographics and other patient data in 2017. Updates on the microbiology, microbiome, and inflammation in patients with bronchiectasis are clarifying the complexities of airway infection in this disease. A consensus definition of 'exacerbation' in bronchiectasis has been agreed upon this year. Reports on novel treatments, including the repurposing of older therapies, have also been published in 2016-2017. A new European guideline for the management of adult bronchiectasis is also now available.

SUMMARY

Bronchiectasis, a resurgent disease, is now being better defined with a rapidly expanding portfolio of demographic, clinical, and therapeutic research and publications.

摘要

目的综述

支气管扩张症曾被认为是一种罕见病,但现在在美国和世界各地的诊断频率都在增加。本综述旨在提供支气管扩张症诊断和治疗方面的最新文献更新。

最新发现

2017 年,两个大型支气管扩张症患者登记处发表了关于人口统计学和其他患者数据的初步报告。对支气管扩张症患者的微生物学、微生物组和炎症的更新,阐明了该疾病气道感染的复杂性。今年还就支气管扩张症“加重”达成了共识定义。2016-2017 年还发表了关于新型治疗方法的报告,包括旧疗法的再利用。目前也有新的欧洲成人支气管扩张症管理指南。

总结

支气管扩张症是一种重新出现的疾病,随着越来越多的人口统计学、临床和治疗研究和出版物的出现,其定义也在不断扩展。

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Bronchiectasis update.支气管扩张症的最新进展。
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引用本文的文献

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Construction of a panoramic mRNA map of adult noncystic fibrosis bronchiectasis and a preliminary study of the underlying molecular mechanisms.构建成人非囊性纤维化支气管扩张症全景 mRNA 图谱及潜在分子机制的初步研究。
Eur J Med Res. 2024 Aug 10;29(1):413. doi: 10.1186/s40001-024-01994-2.
2
Incremental Load Respiratory Muscle Training Improves Respiratory Muscle Strength and Pulmonary Function in Children with Bronchiectasis.递增负荷呼吸肌训练可改善支气管扩张症患儿的呼吸肌力量和肺功能。
Can Respir J. 2024 May 23;2024:8884030. doi: 10.1155/2024/8884030. eCollection 2024.
3
Case report: A case of mutations causing pendred syndrome and non-cystic fibrosis bronchiectasis.
病例报告:一例由突变导致的彭德莱德综合征和非囊性纤维化支气管扩张症。
Front Pediatr. 2023 Jan 9;10:1077878. doi: 10.3389/fped.2022.1077878. eCollection 2022.
4
Exacerbation of bronchiectasis by complicating COVID-19 disease: A case report.新型冠状病毒肺炎并发支气管扩张症急性加重:一例报告
Exp Ther Med. 2021 Dec;22(6):1452. doi: 10.3892/etm.2021.10887. Epub 2021 Oct 15.
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and Respiratory Diseases: 2021 Update.与呼吸系统疾病:2021年更新。 (你提供的原文似乎不完整,“and”前面应该还有相关内容,这是按照现有内容直接翻译的结果)
Microorganisms. 2021 Sep 26;9(10):2033. doi: 10.3390/microorganisms9102033.
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Bronchiectasis-Could Immunonutrition Have a Role to Play in Future Management?支气管扩张症——免疫营养在未来治疗中能发挥作用吗?
Front Nutr. 2021 Apr 29;8:652410. doi: 10.3389/fnut.2021.652410. eCollection 2021.
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Bronchiectasis in Primary Antibody Deficiencies: A Multidisciplinary Approach.原发性抗体缺陷病相关支气管扩张症:多学科方法
Front Immunol. 2020 Mar 31;11:522. doi: 10.3389/fimmu.2020.00522. eCollection 2020.