Matthews-Brzozowska Teresa, Hojan-Jezierska Dorota, Loba Wawrzyniec, Worona Marta, Matthews-Brzozowski Artur
Chair and Department of Maxillofacial Orthopaedics and Orthodontics, Poznan University of Medical Sciences, Poznan, Poland.
Department of Hearing Healthcare Profession, Poznan University of Medical Sciences, Poznan, Poland.
Open Med (Wars). 2018 Mar 1;13:1-8. doi: 10.1515/med-2018-0001. eCollection 2018.
A review of numerous case reports was made, in order to demonstrate the possibilities for treatment of dental disorders in patients with Cleidocranial dysplasia (CCD). In this paper, our own report, including a diagnosis of the effect on the auditory system, is presented. In addition to the triad of CCD symptoms that include hypoplastic or aplastic clavicles, impacted and supernumerary teeth, delayed closure of fontanelles and cranial sutures, impairment of the hearing system resulting in conductive hearing loss also occurs. Our own report is based on the case of a 12-year-old CCD patient, in whom Cone Beam Computed Tomography (CBCT) revealed the presence of 12 supernumerary teeth. Furthermore, a clinical examination pointed to the presence of retained deciduous teeth and a delayed eruption of permanent teeth. Orthodontic-surgical procedures were implemented, in accordance with the literature. During the course of the orthodontic treatment, a decrease in auditory sensitivity was observed, for which reason hearing tests were also performed. Conductive hearing loss was detected. As such, it is important to remember that in such cases, auditory check-ups need to be performed between the many surgical and orthodontic interventions, which usually last a few years.
为了证明锁骨颅骨发育不全(CCD)患者牙齿疾病的治疗可能性,我们对大量病例报告进行了回顾。本文展示了我们自己的报告,其中包括对听觉系统影响的诊断。除了CCD的三联征症状,即锁骨发育不全或缺失、阻生牙和多生牙、囟门和颅缝闭合延迟外,还会出现导致传导性听力损失的听力系统损害。我们自己的报告基于一名12岁CCD患者的病例,该患者的锥形束计算机断层扫描(CBCT)显示有12颗多生牙。此外,临床检查发现存在乳牙滞留和恒牙萌出延迟。根据文献实施了正畸-外科手术。在正畸治疗过程中,观察到听觉敏感性下降,因此还进行了听力测试。检测到传导性听力损失。因此,重要的是要记住,在这种情况下,需要在通常持续数年的许多外科和正畸干预之间进行听力检查。