a Departement of Modern Sciences and Technologies, Faculty of Medicine , Mashhad University of Medical Sciences , Mashhad , Iran.
b Metabolic Syndrome Research Centre, School of Medicine , Mashhad University of Medical Sciences , Mashhad , Iran.
Ann Med. 2018 Jun;50(4):303-311. doi: 10.1080/07853890.2018.1457795. Epub 2018 Apr 10.
Hypercholesterolemia is a pathological condition which has been reported in 39% of the worlds' adult population. We aimed to review molecular aspects of current and novel therapeutic approaches based on low-density lipoprotein cholesterol lowering strategies. Pathogenic mutations in the LDLR, ApoB, PCSK9 and LDLRAP genes cause deficient clearance of circulating low-density lipoprotein cholesterol particles via hepatic LDL receptor. This leads to increased plasma LDL cholesterol levels from birth, which can cause LDL depositions in the arterial walls. Ultimately, it progresses to atherosclerosis and an increased risk of premature cardiovascular diseases. Currently, statins, Ezetimibe, Bile acid sequestrants and PCSK9 inhibitors are the main therapeutic agents for the treatment of hypercholesterolemia. Moreover, novel RNA-based therapy had a strong impact on therapeutic strategies in recent decades. Additional development in understanding of the molecular basis of hypercholesterolemia will provide opportunities for the development of targeted therapy in the near future. Key Messages The most common genes involved in hypercholesterolemia are LDLR, PCSK9 and ApoB. Pharmacogenetic effects are typically constrained to pathways closely related to the pharmacodynamics and pharmacokinetics. Change in lifestyle and diet along with treatment of the underlying disease and drug therapy are the current therapeutic strategies.
高胆固醇血症是一种已在全球 39%的成年人中报道的病理状况。我们旨在综述基于降低低密度脂蛋白胆固醇策略的当前和新型治疗方法的分子方面。LDLR、ApoB、PCSK9 和 LDLRAP 基因的致病性突变导致通过肝 LDL 受体清除循环中的低密度脂蛋白胆固醇颗粒的能力受损。这会导致从出生开始血浆 LDL 胆固醇水平升高,从而导致 LDL 在动脉壁中沉积。最终,它会进展为动脉粥样硬化和过早发生心血管疾病的风险增加。目前,他汀类药物、依折麦布、胆汁酸螯合剂和 PCSK9 抑制剂是治疗高胆固醇血症的主要治疗药物。此外,新型 RNA 疗法在近几十年来对治疗策略产生了重大影响。对高胆固醇血症分子基础的理解的进一步发展将为未来靶向治疗的发展提供机会。
与高胆固醇血症相关的最常见基因是 LDLR、PCSK9 和 ApoB。
药物遗传学效应通常局限于与药效学和药代动力学密切相关的途径。
改变生活方式和饮食以及治疗基础疾病和药物治疗是当前的治疗策略。