Kim Sang Jin, Yang Jianlong, Liu Gangjun, Huang David, Campbell J Peter
Ophthalmic Surg Lasers Imaging Retina. 2018 Apr 1;49(4):273-275. doi: 10.3928/23258160-20180329-11.
Incontinentia pigmenti (IP) is a rare X-linked dominant disorder that can cause retinal nonperfusion, neovascularization, and retinal detachment. Evaluation of the peripheral retinal vasculature and appropriate treatment can reduce the risk of blindness. The authors report the use of a handheld prototype optical coherence tomography angiography (OCTA) and ultra-widefield OCT (UWF-OCT) during exam under anesthesia of a 2-year-old with a history of severe early onset IP. UWF-OCT and OCTA may be used as noninvasive imaging modalities for IP and similar retinal vascular disorders in supine young children. [Ophthalmic Surg Lasers Imaging Retina. 2018;49:273-275.].
色素失禁症（IP）是一种罕见的X连锁显性疾病，可导致视网膜无灌注、新生血管形成和视网膜脱离。评估周边视网膜血管系统并进行适当治疗可降低失明风险。作者报告了在一名有严重早发性IP病史的2岁儿童麻醉检查期间使用手持式光学相干断层扫描血管造影（OCTA）原型和超广角光学相干断层扫描（UWF-OCT）的情况。UWF-OCT和OCTA可用作仰卧位幼儿IP及类似视网膜血管疾病的非侵入性成像方式。[《眼科手术、激光与视网膜成像》。2018年；49:273 - 275。]
